American Thoracic Society International Conference
Where today’s science meets tomorrow’s care
TM
Rare Lung Disease Guide May 13-May 18, 2016
San Francisco, California conference.thoracic.org
Zea Borok, MD University of Southern California, Los Angeles ATS 2016 International Conference Chair
May 2016 Dear Colleagues: The scope of the American Thoracic Society is amazingly broad – covering pulmonary, critical care, and sleep medicine. Our challenge as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees and patients may not be prominently featured in the program each year. This is the case with some of rare lung diseases. With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2016, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations. In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on uncommon respiratory diseases has produced some of the most exciting discoveries in pulmonary medicine. “Insights gained from uncommon lung diseases often shed light on the more common ones.” The definition of a rare disease by its prevalence varies by country. In the European Union, for instance, it is defined as a disease that affects fewer than 1 in 2,000 while in the United States it is a disease that affects fewer than 1 in 200,000. This guide was compiled by a small group of ATS Members who studied the ATS 2016 abstracts – authors requested to be considered for inclusion. Many thanks to Dr. Frank McCormack, Dr. Lisa Young, Dr. Jonathan Kropski, Dr. Nishant Gupta and Mr. Jack Kelly for their assistance with compiling this resource. There are a number of patient advocacy groups that are exhibiting at ATS 2016. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in BOLD are members of the ATS Public Advisory Roundtable and can all be found in PAR ROW, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work, here: http://www.thoracic.org/patients/par/. Alpha-1 Foundation – Booth 1028 ARDS Foundation – Booth 506 Children’s Interstitial Lung Disease Foundation (CHILD) – Booth 993 Foundation for Sarcoidosis Research – Booth 1026 The LAM Foundation – Booth 1032 Lung Transplant Foundation – Booth 927 Lymphangiomatosis and Gorham’s Disease Alliance – Booth 1126 Sincerely,
Zea Borok, MD
NTM Info & Research, Inc. – Booth 1027 Primary Ciliary Dyskinesia Foundation – Booth 1030 Pulmonary Fibrosis Foundation – Booth 2111 Pulmonary Hypertension Association – Booth 1128 Rare Lung Diseases Consortium – Booth 1343 Relapsing Polychondritis Awareness and Support Foundation, Inc. – Booth 1843 Scleroderma Foundation – Booth 1029
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Acute Chest Syndrome in Patient with HB SE Sickle Cell Crisis Sunday, May 15, 2016
P572 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Use of V-V ECMO as a Novel Therapy for Severe Acute Chest Syndrome with Diffuse Alveolar Hemorrhage
A54: Critical Care Case Reports: Acute Hypoxemic Respiratory Failure/ARDS
Area E, Hall D (North Building, Lower Level), Moscone Center
120 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Acute Fibrinous and Organizing Pneumonia: A Newly Recognized, but Poorly Understood Disease
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
P1240 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Cardiovascular Risk and Lung Disease Severity in Alpha 1 Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1241 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Prevalence and Nature of Liver Involvement in Patients with PiZZEmphysema, Candidates for Lung Transplantation
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1242 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Effect of Alpha-1 Proteinase Inhibitor (A1-PI) Therapy on Changes in Regional Lung Density: A Post-Hoc Analysis of the RAPID Trial
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1243 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Relationship Between Changes in CT-Measured Lung Density and Lung Volume in Severe Alpha-1 Antitrypsin Deficiency: Post-Hoc Analysis of the RAPID Trial
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1244 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rate of FEV1 Decline in Never-Smoking Alpha-1 Antitrypsin Deficiency Patients with and Without Small Airways Disease
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1245 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Health Status in Never-Smoking Alpha-1 Antitrypsin Deficiency Patients With and Without Airflow Obstruction
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1247 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Serum Proteins Associated with Radiographic Emphysema and Its Progression in Severe Alpha-1 Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1248 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Serum Desmosine, Isodesmosine and Emphysema in Spirometrically Mild PiZZ Alpha-1 Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1249 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Impact of Augmentation Treatment in Alpha-1 Deficiency Patients on Lung Transplantation Result
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1250 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Liver Fibrosis in Alpha 1 Antitrypsin Deficiency-Related Lung Disease
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
Alpha-1 Antitrypsin Deficiency Sunday, May 15, 2016
1
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P1251 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Osteoporosis and Osteopenia in COPD Alpha-1 Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1252 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Demographics and Clinical Profile of Patients with Alpha-1 Antitrypsin Deficiency PiMS Genotype Started on Augmentation Therapy
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1253 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Improving Survival Among ZZ Patients in the AlphaNet Program
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1254 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Differences Between ZZ and SZ Patients in the AlphaNet Program
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1255 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Gender Differences in Alpha-1-Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1256 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rare Alpha-1 Antitrypsin Mutations Detected in Ireland
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1257 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Irish Alpha-1 Antitrypsin Deficiency National Targeted Detection Programme
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1258 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Alpha-1 Antitrypsin Deficiency in Romania - First Steps (Results of First Three Years of Screening)
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1259 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Alpha-1 Antitrypsin Level Increase During an Inflammatory State: A Potential Cause of Missed Diagnosis in Alpha-1 Antitrypsin Deficiency
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1260 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Alpha-1 Antitrypsin Deficiency - Do We Really Understand It? Case Presentations
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1263 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Impact of AATD Patient Management Program on Health-Related Outcomes and Costs
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1264 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Evaluation of Strategies for Comprehensive Diagnostic Testing for A1Antitrypsin Deficiency that Include Quantitative Isoelectric Focusing and DNA Sequencing
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1265 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Elephant in the Room
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P1266 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Generating a Novel Model of Alpha-1 Antitrypsin Deficiency Pathogenesis by Deriving Type II Alveolar Cells from Pluripotent Stem Cells
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
2
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P1268 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Effects of Recombinant Alpha1-Antitrypsin IgG1 Fc-Fusion Protein (AAT-Fc) in Experimental Emphysema
A43: Alpha-1-Antitrypsin Deficiency
Area L, Hall D (North Building, Lower Level), Moscone Center
P247 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Web-Based Approach for Awareness and Management of Alpha1Antitryspin Deficiency
A58: Epidemiology Of COPD And Lung Cancer
Area C, Hall D (North Building, Lower Level), Moscone Center
309 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Alpha-1 Clinical Demographics and Outcomes: Data from the Alpha-1 Therapy, Evaluation and Research (AL1TER) Patient Registry Program
A102: Highlights In Patient-Centered Research: Methods And Outcomes
Room 309 (South Building, Esplanade Level), Moscone Center
P140 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Overview of Multicenter Genomic Research in Alpha-1 Antitrypsin Deficiency and Sarcoidosis (GRADS) and Biorepository
B31: Alpha-1 Antitrypsin Deficiency
Area B, Hall D (North Building, Lower Level), Moscone Center
P164 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Alveolar Macrophage-Mediated Efferocytosis in Alpha-1 Antitrypsin Deficiency
B32: Alveolar Macrophage Biology
Area B, Hall D (North Building, Lower Level), Moscone Center
P1242 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Resolution of Sequential Mycobacterial Infections Associated with Alpha-1Antiprotease Therapy
B49: Non-Tuberculous Mycobacterial Disease And Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P1017 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
miR-199a-5p, miR-598 and miR-320a Are Regulated by NF?B and Decreased in Monocytes of ZZ Individuals Receiving Alpha-1 Antitrypsin Augmentation Therapy
B59: Novel Genes And Gene Effects In Copd
Area H, Hall D (North Building, Lower Level), Moscone Center
P1007 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Molecular Characterization of Novel Rare Variants of SERPINA1 Gene in Alpha-1 Antitrypsin Deficiency Patients from Spain
B59: Novel Genes And Gene Effects In COPD
Area H, Hall D (North Building, Lower Level), Moscone Center
107 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Rare SERPINA1 Variants in the Multi-Ethnic SPIROMICS Population
B105: COPD: Epidemiology And Genetics
Room 133 (North Building, Lower Level), Moscone Center
P635 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Exercise and Pulmonary Rehabilitation Participation Among Patients with Alpha-1 Antitrypsin Deficiency
C59: Topics On Self-Management And Supportive Care Across The Spectrum Of Chronic Respiratory Conditions
Area F, Hall D (North Building, Lower Level), Moscone Center
P1295 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Alpha-1 Antitrypsin Decreases Pro-Inflammatory Monocyte-Endothelial Cells Interactions Via Fractalkine Axis
C68: Immune Cell Interactions In COPD
Area L, Hall D (North Building, Lower Level), Moscone Center
P1314 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
In Vivo Imaging of Polymers in Alpha-1 Antitrypsin Deficiency
C69: Here’s Looking At You: Imaging Studies In COPD
Area L, Hall D (North Building, Lower Level), Moscone Center
522 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Macrophages from Patients with Z Mutation in Antitrypsin Have Increased Proteolytic Activity on Extracellular Matrix Through Matriptase-MMP-14
C107: Immunity, Exacerbation And Immune Cell Function In COPD
Room 2014 (West Building, Level 2), Moscone Center
Monday, May 16, 2016
Tuesday, May 17, 2016
3
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
P702 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary AA Amyloidosis Presenting as Interstitial Infiltrates in Rheumatoid Arthritis
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1457 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Unusual Case of Severe Pulmonary Hypertension Due to Pulmonary Amyloidosis Along with Cardiac Amyloidosis Presenting with Atypical Features in the Same Patient
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
P396 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Localized Tracheobronchial Amyloidosis Presenting with Massive Hemoptysis in an Intubated, Critically Ill Patient
B37: Interventional Pulmonary Medicine: Cool Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P296 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pleural Involvement in Extensive Bilateral Primary Nodular Parenchymal Amyloidosis: An Incidentaloma
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P341 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Elderly Man with Shortness of Breath: A Case of Primary Pulmonary Amyloidosis
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P345 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Presentation of Isolated Pulmonary Amyloidosis Mimicking Malignancy
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P452 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Cystic Lung Disease
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P282 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Nodular Pulmonary Amyloid Presenting with Hemoptysis
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Disease: Case Reports Lower Level), Moscone Center
P286 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Immunoglobulin Light Chain Amyloidosis Presenting as Supraglottic Mass, Bronchiectasis, and Cystic Lung Disease
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Disease: Case Reports Lower Level), Moscone Center
P299 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Amyloidosis: A Rare Presentation of a Rare Disease
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Disease: Case Reports Lower Level), Moscone Center
116 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Pulmonary Amyloidosis: Clinicopathologic Correlation in an Autopsy Series of Amyloidosis
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
P701 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Zebras Have Hooves Too: A Case of Granulomatosis with Polyangiitis
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P709 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Important of Complete Evaluation of a Patient with Recurrent Diffuse Alveolar Hemorrhage: A Case Study
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
Amyloidosis Sunday, May 15, 2016
Monday, May 16, 2016
Tuesday, May 17, 2016
ANCA Associated Vasculitis Sunday, May 15, 2016
4
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P729 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Patients with Difficult to Control Eosinophilic Granulomatosis with Polyangiitis of a Vasculitis Clinical Center in Sao Paulo, Brazil
A39: Eosinophilic Airways Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1234 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
HLA- Genotyping and Clinical Manifestation in Patients with Granulomatosis with Polyangiitis
A42: Autoimmune Myositis, Antisynthetase, Scleroderma, And IPAF
Area L, Hall D (North Building, Lower Level), Moscone Center
P1278 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Case-Control Study of HLA Region in Brazilian Carriers of Granulomatosis with Polyangiitis (Wegener’s)
A44: Drug Induced And Rare Lung Disease
Area L, Hall D (North Building, Lower Level), Moscone Center
P126 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Nasal Disease, a Common Comorbidity in Patients with Chronic Severe Asthma (CSA) and Eosinophilic Granulomatosis with Poliangiitis (EGPA)
A50: Asthma: Observational Studies
Area A, Hall D (North Building, Lower Level), Moscone Center
P335 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rare Case of ANCA Vasculitis with Alveolar Hemorrhage in Non- Hodgkin Lymphoma
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P116 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Lung Perfusion Evaluation in Patients with Stable Granulomatosis with Polyangiitis
B55: Reason To Believe: Clinical PH Studies
Area A, Hall D (North Building, Lower Level), Moscone Center
106 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Radiological Versus Histological Diagnosis in Antisynthetase Associated Interstitial Lung Disease
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
107 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Additional Clinical Signs and Symptoms Develop in Patients with Antisynthetase Syndrome-Associated Interstitial Lung Disease Followed Over 24 Months
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
P711 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rituximab - Respiratory Rescue; Salvage Therapy in Acute Antisynthetase Syndrome
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1222 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mycophenolate Mofetil (MMF) as Initial Treatment in Antisynthetase Syndrome - A Case Report
A42: Autoimmune Myositis, Antisynthetase, Scleroderma, And IPAF
Area L, Hall D (North Building, Lower Level), Moscone Center
P1223 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Retrospective Analysis of Twelve Patients with Anti-Synthetase Syndrome Mayo Clinic Experience
A42: Autoimmune Myositis, Antisynthetase, Scleroderma, And IPAF
Area L, Hall D (North Building, Lower Level), Moscone Center
P1326 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Curious Case of Acute Respiratory Failure - Anti-Synthetase Syndrome
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P1328 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Flare of Anti-Synthetase Interstitial Lung Disease with Cessation of Immunosuppression
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
Anti-Synthetase Associated ILD Sunday, May 15, 2016
5
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P1329 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Infliximab for Treatment of Anti PL-12 Antisynthetase Syndrome: Misdiagnosis Led to New Potential Treatment for Rare Disease
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P207 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Retrospective Cohort Analysis of Anti-Jo Associated Lung Disease
C37: Pulmonary Fibrosis
Area B, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
9:00 am-11:00 am; Oral Presenation 10:00 am
Azathioprine for Antisynthetase-Associated Interstitial Lung Disease
D15: New Therapies In ILD
Room 306/308 (South Building, Esplanade Level), Moscone Center
Arterio-Venous Malformations Monday, May 16, 2016
P109 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Clinical Significance of Detecting Pulmonary Arterio-Venous Malformations with Chest Radiographs
B55: Reason To Believe: Clinical PH Studies
Area A, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P586 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Diagnosis and Management of Sporadic Pulmonary Arteriovenous Malformation Not Associated with Hereditary Hemorrhagic Telangiectasia
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P994 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Arteriovenous Malformations in Non-Hereditary Hemorrhagic Telangiectasia Patients: A 15-Year Retrospective Study
D53: The Promised Land: Clinical Studies In Pulmonary Hypertension
Area H, Hall D (North Building, Lower Level), Moscone Center
522 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Recurrent Hemoptysis in a Teen Boy with a Ciliary Motility Disorder and a Pulmonary Vascular Malformation Occult on Contrast Enhanced CT.
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Atypical Multifocal Pulmonary Carcinoid Tumor: A Case Report of a Very Rare Neoplasm
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
A Case of Behcet’s Disease Presenting with Right Atrial Thrombus and Pulmonary Embolism
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Bilateral Synchronous Pulmonary Carcinoid Tumors Treated with Staged Segmentectomy
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Atypical Multifocal Pulmonary Carcinoid Tumor Wednesday, May 18, 2016
301 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Behcet’s Disease Sunday, May 15, 2016
P1464 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Bilateral Synchronous Carcinoid Tumor of the Lung Wednesday, May 18, 2016
302 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
6
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
P256 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Concurrent Birt-Hogg-Dube Syndrome and Sarcoidosis
C41: Sarcoidosis: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
107 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung Diseases
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
108 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting with Spontaneous Pneumothorax is Cost Effective
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
111 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Total Covering Technique for Recurrent Pneumothorax in Patients of Birt-Hogg-Dube Syndrome
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
A 17-Year-Old Male Presenting with Recurrent Pneumonias from a Primary Pulmonary Tumor
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
Birt-Hogg-Dube Syndrome Tuesday, May 17, 2016
Bronchial Pulmonary Carcinoid Tumor Wednesday, May 18, 2016
P552 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Bronchiolitis Obliterans and Cryptogenic Organizing Pneumonias 120 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Acute Fibrinous and Organizing Pneumonia: A Newly Recognized, but Poorly Understood Disease
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
P1313 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Unusual Presentation of Organizing Pneumonia in Primary Sjogren’s Syndrome
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P337 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Unexplained Dyspnea in a Non-Smoker: Think Outside the Box
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P336 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Diagnostic Dilemma with Crazy Paving Pattern
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P583 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Delayed Diagnosis of Post Infectious Bronchiolitis Obliterans Associated with RSV
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
113 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Organizing Pneumonia in Myelodysplastic Syndrome: A Case Series
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
Sunday, May 15, 2016
7
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Wednesday, May 18, 2016
P545 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Complications of Stevens Johnson Syndrome: A Single Center Experience
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P557 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Bronchiolitis Obliterans Organizing Pneumonia Complicating Acute Lymphoblastic Leukemia in Children
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
An Uncommon Congenital Anomaly Mimicking Mediastinal Carcinoma
B37: Interventional Pulmonary Medicine: Cool Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Bronchogenic Cysts Monday, May 16, 2016
P392 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Castleman Disease Tuesday, May 17, 2016
P245 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Castleman Disease Associated Diffuse Parenchymal Lung Disease: A Retrospective Analysis of 21 Cases in a Tertiary Chinese Hospital
C40: Sarcoidosis: Understanding This Multi-System Disorder
Area C, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P328 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Multicentric Castleman’s Disease Without Apparent Mediastinal Lymphadenopathy and a Review of the Japanese Literature
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
421 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
5-ASA Treatment in Chronic Beryllium Disease
B24: Occupational Medicine
Room 2010/2012 (West Building, Level 2), Moscone Center
422 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
The Role of JAK2 in Chronic Beryllium Disease
B24: Occupational Medicine
Room 2010/2012 (West Building, Level 2), Moscone Center
Cancer Is Not Always the Answer
D48: Lung Infection Case Reports I: Fungal Infections
Area G, Hall D (North Building, Lower Level), Moscone Center
919 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Dendritic Cell-Mediated Lung Injury in Response to Aspergillus in Chronic Granulomatous Disease: Protective Role of Neutrophil-Derived Reactive Oxygen Species
B106: Cellular/Molecular Mechanisms And Translational Aspects Of Respiratory Tract Infections
Room 3014 (West Building, Level 3), Moscone Center
P306 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Chylothorax: The Milky Truth of Cirrhosis
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Chronic Beryllium Disease Monday, May 16, 2016
Chronic Cavitary Histoplasmosis Wednesday, May 18, 2016
P767 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Chronic Granulomatous Disease Monday, May 16, 2016 Chylothorax Monday, May 16, 2016
8
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Monday, May 16, 2016
P340 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Massive Bilateral Chylothorax
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Congenital Central Hypoventilation Syndrome Sunday, May 15, 2016
805 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Intelligent Volume-Assured Pressured Support (iVAPS) for the Treatment of Pediatric Congenital Central Hypoventilation Syndrome
A27: Advances In Pediatric Sleep
Room 3011 (West Building, Level 3), Moscone Center
Tuesday, May 17, 2016
9:00 am-11:00 am; Oral Presentation 10:15 am
Does High Altitude Cause Hypoventilation in Patients with Congenital Central Hypoventilation Syndrome?
C19: From Genes To Motor Neurons: Advances In Control Of Breathing
Room 2001/2003 (West Building, Level 2), Moscone Center
P574 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Children Affected by Congenital Central Hypoventilation Syndrome: Decannulation and Non Invasive Ventilation
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Nutritional Follow-Up of Congenital Diaphragmatic Hernia Survivors - The Sydney Children’s Hospital Experience
D25: Neonatal Lung Diseases: From Bench To Babies
Room 3011 (West Building, Level 3), Moscone Center
Congenital Diaphragmatic Hernia Wednesday, May 18, 2016
822 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Congenital Myotonic Dystrophy Tuesday, May 17, 2016
P592 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Successful Use of Non Invasive Ventilation in a Child Affected by Congenital C62: Pediatric Cases I Myotonic Dystrophy Syndrome
Area E, Hall D (North Building, Lower Level), Moscone Center
Congenital Pulmonary Airway Malformation (CPAM) with Malignant Transformation
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Cystic Lung Disease in Adult Polycystic Kidney Disease
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
Congenital Pulmonary Adenomatous Malformations Wednesday, May 18, 2016
309 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Cystic Lung Disease in Adult Dominant Polycystic Kidney Disease Tuesday, May 17, 2016
P444 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Cystic Teratoma of the Pleura Monday, May 16, 2016
P319 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Intrapleural Benign Mature Cystic Teratoma
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P53 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Benign Metastasizing Leiomyoma
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
9
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Extreme Tachypnea in a Neonate - A Case of Diaphragmatic Flutter with an Interesting Genetic Outcome
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Diaphragmatic Flutter Wednesday, May 18, 2016
513 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) Monday, May 16, 2016
Tuesday, May 17, 2016
P478 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
All that Wheezes Is Not Asthma but More so if Chest CT Shows Lung Nodules
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P564 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Unsual Cause for Multiple Pulmonary Nodules
B66: Lung Cancer Screening And Nodule Evaluation
Area E, Hall D (North Building, Lower Level), Moscone Center
P283 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia Presenting as Usual Interstitial Pneumonia
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P88 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
DIPNECH a Rare Cause of Obstructive Airway Disease
C81: Unusual Presentations Of Lung Cancer: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Is Diffuse Panbronchiolitis Ionizing Radiation Related?
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Miliary Pattern and No Complaints
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P730 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Long-Term Outcome and Prognostic Factors of Chronic Eosinophilic Pneumonia: Fujiyama Cohort Study
A39: Eosinophilic Airways Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1297 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Sun Damage or Lung Damage: Heliocare? (Polypodium Leucotomas)Induced Eosinophilic Pneumonitis
A46: Lung Disease Due To OTC And Illicits: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P327 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Wheezing with Yellow Eyes: A Case of Chronic Eosinophillic Pneumonia
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P331 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Atypical Presentation of Chronic Eosinophilic Pneumonia with Concomitant Mycobacterium Avium Infection
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Diffuse Panbronchiolitis Tuesday, May 17, 2016
P334 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Diffuse Pulmonary Meningotheliomatosis Tuesday, May 17, 2016
P330 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Eosinophilic Pneumonia Sunday, May 15, 2016
Tuesday, May 17, 2016
10
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
P350 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Chronic Eosinophilic Pneumonia Complicated by Methicillin-Resistant Staphylococcus Aureus
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P569 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Eosinophilic Pneumonia
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
P574 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Chronic Eosinophilic Pneumonia in a 15-Year-Old Girl with Persistent Cough
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
A Rare and Interesting Cause of Pulmonary Nodules: A Case of Epithelioid Hemangioendothelioma
B66: Lung Cancer Screening And Nodule Evaluation
Area E, Hall D (North Building, Lower Level), Moscone Center
Metastatic Epithelioid Trophoblastic Tumor to the Lungs
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Erasmus Syndrome in a Patient Evaluated for Pulmonary Hypertension
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Unusual Presentation of Erdheim-Chester Disease with Hemoptysis and Dyspnea as the Initial Chief Complaint
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Solitary Extramedullary Plasmacytoma of the Trachea: A Case Report and Review of the Literature
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Respiratory Characteristics in Patients with Familial Dysautonomia
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
Epithelioid Hemangioepithelioma Monday, May 16, 2016
P560 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Epithelioid Trophoblastic Tumor Tuesday, May 17, 2016
P55 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Erasmus Syndrome Tuesday, May 17, 2016
P322 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Erdheim-Chester Disease Tuesday, May 17, 2016
P281 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Extramedullary Plasmacytoma Tuesday, May 17, 2016
P49 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Familial Dysautonomia Wednesday, May 18, 2016
P516 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Fibrosing Mediastinitis Wednesday, May 18, 2016
P773 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Healing and Hardening: Focal Fibrosing Mediastinitis Due to Histoplasmosis D48: Lung Infection Case Reports I: Fungal Infections
Area G, Hall D (North Building, Lower Level), Moscone Center
P774 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Fibrosing Mediastinitis
Area G, Hall D (North Building, Lower Level), Moscone Center
D48: Lung Infection Case Reports I: Fungal Infections
11
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Ground Glass Nodules and Cough in an Individual with Common Variable Immunodeficiency
B34: Case Report In Immunodeficiences And Allergy
Area B, Hall D (North Building, Lower Level), Moscone Center
Don’t Blame the Birds
A46: Lung Disease Due To OTC And Illicits: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Follicular Bronchiolitis in Common Variable Immunodeficiency Monday, May 16, 2016
P186 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Foreign Body Granulomatosis Sunday, May 15, 2016
P1309 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Giant Cell Interstitial Pneumonia Sunday, May 15, 2016
P1356 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Giant Cell Interstitial Pneumonitis (GIP) as a Rare Manifestation of Chronic Nitrofurantoin Lung Toxicity
A48: Conventional Drug Associated Lung Disease
Area L, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P136 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Giant Cell Interstitial Pneumonia in a Patient with World Trade Center Dust Exposure
D46: Case Reports In Environmental And Occupational Health
Area B, Hall D (North Building, Lower Level), Moscone Center
P185 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Japanese Patient Diagnosed Good Syndrome with Prolonged Time After Thymectomy
B34: Case Report In Immunodeficiences And Allergy
Area B, Hall D (North Building, Lower Level), Moscone Center
P191 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Two Tumours, Neuropathy, Infections
B34: Case Report In Immunodeficiences And Allergy
Area B, Hall D (North Building, Lower Level), Moscone Center
P73 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Granular Cell Tumor: A Case of a Rare Tumor with an Unusual Location and Presentation
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
P102 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Coexistent Pulmonary Granular Cell Tumor and Adenocarcinoma of the Lung with Pulmonary Tuberculosis
C81: Unusual Presentations Of Lung Cancer: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Good Syndrome Monday, May 16, 2016
Granular Cell Tumor Tuesday, May 17, 2016
Granulomatous-Lymphocytic Interstitial Lung Disease Tuesday, May 17, 2016
P290 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Granulomatous-Lymphocytic Interstitial Lung Disease as an Early Manifestation of Common Variable Immunodeficiency: A Case Report
Hereditary Hemorrhagic Telangiectasia (Osler-Weber-Rendu Syndrome) Sunday, May 15, 2016
A1460 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Two Rare Conditions Linked by an Activin Receptor-Like Kinase 1 (ALK-1) Mutation
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P52 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Hereditary Hemorrhagic Telangiectasia (Rendu-Osler-Weber Syndrome): Unusual Presentation and Follow Up with CPET
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
12
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
P582 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Worsening Hypoxemia in an 11-Year-Old with Hereditary Hemorrhagic Telangiectasia (HHT)
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
P420 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Epithelial Nox4 Contributes to Fibrotic Susceptibility in Hermansky-Pudlak Syndrome Mice
A73: Lung Fibrosis: New Directions To Inform The Future
Area D, Hall D (North Building, Lower Level), Moscone Center
P423 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Chitinase 3-Like-1 and Its Receptors in Hermansky-Pudlak SyndromeAssociated Lung Disease
A73: Lung Fibrosis: New Directions To Inform The Future
Area D, Hall D (North Building, Lower Level), Moscone Center
P444 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Limp2 Mediates Prdx6 Delivery to Lamellar Bodies in AP3-Deficient Cell and Mouse Models
A73: Lung Fibrosis: New Directions To Inform The Future
Area D, Hall D (North Building, Lower Level), Moscone Center
P316 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Clinical Dilemma in the Lung Transplant Clinic
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P332 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Unusual Usual Interstitial Pneumonia
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P61 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Missed Case of Rare High-Grade Lung Sarcoma Presenting as Cavitary Pneumonia with Unusual Cutaneous Lesions
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
507 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
An Unusual Cause of Tachypnea and Hypoxemia in an Infant
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Idiopathic Pleuroparenchymal Fibroelastosis and Its Mimickers
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
P696 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case Report of IgG4-Related Disease Masquerading as a 4.1 Centimeter Necrotic Pulmonary Mass with Bilateral Pulmonary Nodules
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P699 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
IgG4 Related Disease in the Pleura Manifested as Weight Loss in an Immunocompromised Patient
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
Hermansky-Pudlak Syndrome Sunday, May 15, 2016
Tuesday, May 17, 2016
High Grade Sarcoma Tuesday, May 17, 2016 Horseshoe Lung Wednesday, May 18, 2016
Idiopathic Pleuroparenchymal Fibroelastosis Sunday, May 15, 2016
124 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
IgG4-Related Disease Sunday, May 15, 2016
13
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P708 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Do Not IGnore G4
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1318 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Fatal Hemoptysis Secondary to Fibro-Inflammatory IgG4- Related Lung Disease: A Case Report
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P1323 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Sclerosing Mediastinitis: The Story Within
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P294 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Putting It All Together-A Challenging Diagnosis of Immunoglobulin G4Related Lung Disease (IgG4RLD)
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
118 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Respiratory Manifestations of IgG4 Related Disease: A Retrospective Analysis of 97 Cases in a Single Chinese Hospital
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
Subpleural Cysts in a Patient with Immune Dysregulation, Polyendrocrinopathy, Enteropathy, X-Linked Syndrome
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Prolonged Tachypnea and Hypoxemia as Presentation of Bare Lymphocyte Syndrome, Type II
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Ulcerative Colitis: Inflammation Beyond the Bowel
A48: Conventional Drug Associated Lung Disease
Area L, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
Immune Dysregulation Syndromes Wednesday, May 18, 2016
504 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Immunodeficiency, Severe Combined Wednesday, May 18, 2016
517 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Inflammatory Bowel Disease Sunday, May 15, 2016
P1360 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Inflammatory Myofibroblastic Tumor of the Lung Tuesday, May 17, 2016
P51 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Inflammatory Myofibroblastic Tumor of the Lung: A Rare Case Report
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Sunday, May 15, 2016
122 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Radiographic and Physiologic Abnormalities in Subjects with MyositisAssociated Interstitial Lung Disease
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
14
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Bombesein Staining May Be a Useful Marker in Idiopathic Interstitial Pneumonias Other Than NEHI
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
Synchronous Intralobar Pulmonary Sequestration and Poorly Differentiated Adenocarcinoma in the Right Lower Lung Lobe
C81: Unusual Presentations Of Lung Cancer: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Kikuchi-Fujimoto Disease: A Refractory Case
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P441 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Diffuse Cystic Lung Disease in A Heavy Smoker: A Rare Case of Pulmonary Langerhans Cell Histiocytosis
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P276 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Atypical Langerhans Cell Histiocytosis Masquerading as Hidradenitis Suppurativa
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
107 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung Diseases
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
108 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting with Spontaneous Pneumothorax is Cost Effective
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
P544 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Langerhans Cell Histiocytosis and Pulmonary Involvement: Long Term Follow Up in 22 Pediatric Patients Having Pulmonary Function Tests
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P563 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Primary Pulmonary Langerhans Cell Hystiocytosis in a Three-Year-Old Patient
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
P564 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Which Is the Better Treatment for Pulmonary Langerhans Cell Histiocytosis in Children?
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
Large Cell Neuroendocrine Carcinoma of the Lung: A Rare Cancer by EBUS Guided Core Needle Biopsy
C79: Multimodality Approaches To Diagnosis And Treatment Of Lung Cancer
Area A, Hall D (North Building, Lower Level), Moscone Center
Interstitial Lung Disease Wednesday, May 18, 2016
P515 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Intralobar Bronchopulmonary Sequestration Tuesday, May 17, 2016
P98 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Kikuchi-Fujimoto Disease Tuesday, May 17, 2016
P312 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Langerhans Cell Histiocytosis Tuesday, May 17, 2016
Wednesday, May 18, 2016
Large Cell Neuroendocrine Carcinoma of the Lung Tuesday, May 17, 2016
P10 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
15
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Leiomyoma, Pulmonary Benign Metastasizing Tuesday, May 17, 2016
P53 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Benign Metastasizing Leiomyoma
C:80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
306 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Pulmonary Benign Metastasizing Leiomyoma: A Case Report
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Leiomyosarcoma Arising from the Right Pulmonary Artery as a Cause for Superior Vena Cava Syndrome: A Case of Dyspnea Not Entirely Explained by Pulmonary Embolus
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
A Rare Cause of Nodular Cystic Disease: Report of Three Cases
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
Atypical Large Hydropneumothorax in the Setting of an Uncommon Lung Neuroendocrine Tumor
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Lung Placental Transmogrification
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Leiomyosarcoma Arising from the Right Pulmonary Artery Wednesday, May 18, 2016
307 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Light Chain Deposition Disease (LCDD) Tuesday, May 17, 2016
106 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Lung Neuroendocrine Tumor Wednesday, May 18, 2016
303 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Lung Placental Transmogrification Monday, May 16, 2016
P480 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Lymphatic Anomaly (Lymphangiomatosis), Lymphangiectasia, and Gorham-Stout Disease Tuesday, May 17, 2016
P309 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Kaposiform Lymphangiomatosis: An Unforeseen Cause of Spontaneous Hemothorax and Episodic Hemoptysis
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P683 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rapamycin Reverses Lymphatic Abnormalities in a Transgenic Mouse Model of Pulmonary Lymphangiectasia
B52: Neonatal Lung Disease: From Bench To Babies
Area F, Hall D (North Building, Lower Level), Moscone Center
P449 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Imatinib Treatment of Lymphangiomatosis
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P579 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Unique Case of Pulmonary Lymphangectasia in a Teenager
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
16
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
P598 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Gorham-Stout Disease in a Young Pregnant Female-A Management Dilemma
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
P41 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Chyloptysis, Hemoptysis, and Chylothorax in a Fifty-Year-Old Woman
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
P1320 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Case Report: Pulmonary Lymphangioleiomyomatosis in a Post-Menopausal Female Patient
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P1497 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
High-Intensity Exercise to Treat a Patient with Tuberous Sclerosis Complex-Lymphangioleiomyomatosis (TSC-LAM)
A69: Pulmonary Rehabilitation In Pulmonary Hypertension, Interstitial Lung Disease, And Other Conditions: What’s New?
Area M, Hall D (North Building, Lower Level), Moscone Center
P1498 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Exercise Training Improves Pulmonary Function and Bone Mineral Density in Women with Lymphangioleiomyomatosis (LAM)
A69: Pulmonary Rehabilitation In Pulmonary Hypertension, Interstitial Lung Disease, And Other Conditions: What’s New?
Area M, Hall D (North Building, Lower Level), Moscone Center
P481 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Expression and Activity of Cathepsin K in Lymphangioleiomyomatosis (LAM)
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P482 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Transcriptomic Differences Associated with TSC2 Gene Expression Loss in Lymphangioleiomyomatosis
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P483 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Lymphangioleiomyomatosis (LAM): Inflammatory Cell Infiltration in Human LAM Lung
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P484 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Myeloid Cell Recruitment in a TSC2-Null Mouse Model of Lymphangioleiomyomatosis (LAM)
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P485 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mesenchymal Tsc2 Deficiency Causes Retarded Lung Alveolarization and Polycystic Kidney Lesion
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P486 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Integrin β5 Implication in the Tumorigenic Potential of TSC-Deficient LAM Cells
A76: LAM: New Biology And New Insights
Area D, Hall D (North Building, Lower Level), Moscone Center
P442 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Sporadic Lymphangioleiomyomatosis with Immune Thrombocytopenia
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P445 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Sporadic Lymphangioleiomyomatosis and Pheochromocytoma: A Case of Neural Crest Cells Gone Awry
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
Lymphangioleiomyomatosis (LAM) Sunday, May 15, 2016
Tuesday, May 17, 2016
17
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
P446 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Sporadic Lymphangioleiomyomatosis Confirmed by Thoracentesis
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P451 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Placental Transmogrification of the Lung Mimicking Lymphangioleiomyomatosis
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
P453 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Lymphangioleiomyomatosis in a Female with a Large Ovarian Cyst
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
101 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Early and Late Onset Adverse Events in LAM Patients Treated with Sirolimus for Two Years
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
102 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Early Intervention with Sirolimus Benefits Mild Lymphangioleiomyomatosis-Related Lung Disease
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
103 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Impact of Pleural Disease on Pulmonary Function Test Results in Patients with Lymphangioleiomyomatosis
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
104 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Reproducibility of FEV1 Measurements in Patients with Lymphangioleiomyomatosis
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
107 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung Diseases
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
108 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting with Spontaneous Pneumothorax is Cost Effective
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
123 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Proapototic Protein Bim Mediates Estrogen-Enhanced Survival in Lymphangioleiomyomatosis
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
124 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Cell-Cell Communication in Lymphangioleiomyomatosis: Microarray Analysis Shows Induction of Chemokines and Fibroblast Growth Factors in LAM Associated Fibroblasts
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
18
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
125 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
CA-125 in Lymphangioleiomyomatosis Correlates with Disease Progression and Sirolimus Therapy
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
9:00 am-11:00 am; Oral Presentation 10:15 am
Functional Improvement in Patients with Lymphangioleiomyomatosis (LAM) After Sirolimus
D15: New Therapies In ILD
Room 306/308 (South Building, Esplanade Level), Moscone Center
Lymphocytic Interstitial Pneumonia Monday, May 16, 2016
P184 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Interstitial Lung Disease Associated with HIV
B34: Case Report In Immunodeficiences And Allergy
Area B, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P310 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Novel Use: Aspira Catheter Connected with Heimlich Valve to Manage Bronchopleural Fistula in Lymphocytic Interstitial Pneumonia Induced Recurrent Spontaneous Pneumothorax
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Sunday, May 15, 2016
P1462 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Unusual Cause of Pulmonary Hypertension and Cor Pulmonale
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P192 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Primary Effusion Lymphoma and Initiation of HAART in a Critically Ill Patient with AIDS
B34: Case Report In Immunodeficiences And Allergy
Area B, Hall D (North Building, Lower Level), Moscone Center
P281 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Unfortunate Manifestation of HHV-8
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P335 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rare Case of ANCA Vasculitis with Alveolar Hemorrhage in Non-Hodgkin Lymphoma
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P558 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Diffuse Pulmonary Nodules: A Tale of Two Diagnoses
B66: Lung Cancer Screening And Nodule Evaluation
Area E, Hall D (North Building, Lower Level), Moscone Center
P326 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Lymphoma and the Lung: A Case of Chronic Consolidation and Multiple Pneumatoceles in Lymphoplasmacytic Lymphoma
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P36 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Primary Pulmonary Extranodal Zone Lymphoma Mimicking Pneumonia
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
P44 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Primary Pulmonary Anaplastic Large Cell Lymphoma Masquerading as Asthma in a Young Woman
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Lymphoma
Tuesday, May 17, 2016
19
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
P46 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
An Unusual Way to Diagnose Intravascular Large B-Cell Lymphoma
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P553 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Hodgkin Lymphoma Presenting with Multiple Cavitary Pulmonary Lesions
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
312 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Tracheal Mucosa Associated Lymphoid Tissue Lymphoma as a Cause of Chronic Cough and Prandial Dyspnea
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
314 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Extranodal NK/T-Cell Lymphoma Masquerading as Limited Granulomatosis with Polyangiitis
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Lymphomatoid Granulomatosis Presenting as Multiple Lung Masses
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Metastasis from a Neurofibroma
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Targeting EphA2 Using miR-302b Encapsulated-eprhin-A1 Conjugated Liposomal Nanoparticles Inhibits Malignant Pleural Mesothelioma Tumor Growth
C110: Mesothelioma And Malignant Pleural Disease: From Bench To Bedside To Community
Room 309 (South Building, Esplanade Level), Moscone Center
Making the ‘Connection’: A Case of Abnormal Connective Tissue
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
All That Glitters Is Not Gold: A Case of Mercury Pneumonitis
A46: Lung Disease Due To OTC And Illicits: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Lymphomatoid Granulomatosis Tuesday, May 17, 2016
P37 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Malignant Peripheral Neural Sheath Tumors to Lungs Wednesday, May 18, 2016
321 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Malignant Pleural Mesothelioma Tuesday, May 17, 2016
320 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Marfan’s Associated Emphysema Monday, May 16, 2016
P359 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mercury Inhalation Pneumonitis Sunday, May 15, 2016
P1300 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
20
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Microscopic Polyangiitis with an Unusual Pulmonary Manifestation and No Renal Involvement
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Successful Treatment of Early Stage Monophasic Pulmonary Synovial Sarcoma with Minimally Invasive Robotic Video-Assisted Lobectomy
C79: Multimodality Approaches To Diagnosis And Treatment Of Lung Cancer
Area A, Hall D (North Building, Lower Level), Moscone Center
P344 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mounier-Kuhn Syndrome: An Unusual Cause of Dyspnea
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P497 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mounier-Kuhn Syndrome and Cystic Fibrosis Coexist in the Same Patient with Chronic Respiratory Failure
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P1237 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mounier-Kuhn Syndrome Presenting with Dysphagia and Weight Loss
B49: Non-Tuberculous Mycobacterial Disease And Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P289 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Tracheobronchomegaly in Mounier-Kuhn Syndrome Mimicking the Cystic Lung Disease Seen in Lymphangioleiomyomatosis
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P556 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Tracheobronchomegaly (Mounier-Kuhn) and Primary Ciliary Dyskinesia
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
A Rare Case of Mucoepidermoid Carcinoma of the Lung
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Multifocal Micronodular Pneumocyte Hyperplasia in a Patient with Tuberous Sclerosis–Stable Chest CT Findings Over 9 Years of Follow Up
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P1327 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
PM-DM Associated Interstitial Lung Disease
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
111 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Short-Term Efficacy of Treatment in Myositis-Associated ILD
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
Microscopic Polyangiitis Sunday, May 15, 2016
P1325 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Monophasic Pulmonary Synovial Sarcoma Tuesday, May 17, 2016
P22 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mounier-Kuhn Syndrome Monday, May 16, 2016
Mucoepidermoid Carcinoma of the Lung Wednesday, May 18, 2016
304 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Multifocal Micronodular Pneumocyte Hyperplasia Tuesday, May 17, 2016
P323 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Myositis-Associated ILD Sunday, May 15, 2016
21
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
122 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Radiographic and Physiologic Abnormalities in Subjects with Myositis-Associated Interstitial Lung Disease
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
2:15 pm-4:15 pm; Oral Presentation 3:00 pm
Contribution of Mutations in Genes Encoding Proteins of the Surfactant Metabolism to Idiopathic Interstitial Pneumonia and Idiopathic Pulmonary Fibrosis in a Cohort of 265 Families
A94: New Insights In IPF
Room 306/308 (South Building, Esplanade Level), Moscone Center
Necrobiotic Pulmonary Nodules Secondary to Crohn’s Disease
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Necrotizing Granulomatous Pulmonary Nodules Sunday, May 15, 2016
P1317 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Neuroendocrine Cell Hyperplasia of Infancy (NEHI) Monday, May 16, 2016
9:00 am-11:00 am; Oral Presentation 9:45 am
Sleeping chILD: Neuroendocrine Cell Hyperplasia of Infancy and Polysomnography
B19: Best Of Pediatrics
Room 3006/3008 (West Building, Level 3), Moscone Center
Wednesday, May 18, 2016
812 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Quantitative Measures of Ground Glass Opacities Correlate with Use of Daytime Oxygen in Neuroendocrine Cell Hyperplasia of Infancy
D25: Neonatal Lung Diseases: From Bench To Babies
Room 3011 (West Building, Level 3), Moscone Center
P514 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Abnormalities in Adults with Familial Neuroendocrine Cell Hyperplasia of Infancy (NEHI)
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
Neurofibromatosis Sunday, May 15, 2016
P1454 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A 45-Year-Old Woman with Neurofibromatosis Type-1-Associated Pulmonary Arterial Hypertension Responsive to Epoprostenol
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P325 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Neurofibromatosis Related Interstitial Lung Disease: Is There a True Relationship?
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Healthcare Use and Costs Among Patients with Non-Cystic Fibrosis Bronchiectasis in the US
B22: Burden Of Pulmonary And Critical Care Medicine: Cost And Utilization
Room 304 (South Building, Esplanade Level), Moscone Center
Refractory Hyperammonemia: A Case Report of a Patient with Adult Onset Ornithine Carbamoyltransferase Deficiency
A57: Critical Care Case Reports: Non-Pulmonary Critical Care
Area H, Hall D (North Building, Lower Level), Moscone Center
Non-Cystic Fibrosis Bronchiectasis Monday, May 16, 2016
201 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Ornithine Carbamoyltransferase Deficiency Sunday, May 15, 2016
P1024 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
22
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Pulmonary Interstitial Lymphoid Hyperplasia and Autoimmune Hemolytic Anemia Successfully Responding to Steroid Sparing Agents in a 3-Year-Old Boy
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Peribronchial Sclerosing Hemangioma with 68Ga Uptakeof DOTATOC PET-CT
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Placental Transmogrification of the Lung Mimicking Lymphangioleiomyomatosis
C42: LAM, Cystic Lung Disease, And Mimics: Case Reports
Area D, Hall D (North Building, Lower Level), Moscone Center
Atypical Plastic Bronchitis Two Decades After Tetralogy of Fallot Repair
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Malignancy Unmasked - A Rare Primary Pleural Angiosarcoma Presenting as a Complex Empyema
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Pediatric Pulmonary Interstitial Lymphoid Hyperplasia Tuesday, May 17, 2016
P578 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Peribronchial Sclerosing Hemangioma Tuesday, May 17, 2016
P77 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Placental Transmogrification of the Lung Tuesday, May 17, 2016
P451 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Plastic Bronchitis Sunday, May 15, 2016
P1451 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pleural Angiosarcoma Monday, May 16, 2016
P275 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pleuroparenchymal Fibroelastosis (PPFE) Sunday, May 15, 2016
113 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Pleuroparenchymal Fibroelastosis (PPFE) Predicts Survival in Idiopathic Pulmonary Fibrosis (IPF)
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P315 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Functional Respiratory Imaging View on Idiopathic Pleuroparenchymal Fibroelastosis
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
P138 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Pleuroparynchemal Fibroelastosis Due to Long-Term Silica Exposure
D46: Case Reports In Environmental And Occupational Health
Area B, Hall D (North Building, Lower Level), Moscone Center
The Utility of Endobronchial Ultrasound in the Diagnosis of Recurrent Pleuropulmonary Synovial Sarcoma
C79: Multimodality Approaches To Diagnosis And Treatment Of Lung Cancer
Area A, Hall D (North Building, Lower Level), Moscone Center
Pleuropulmonary Synovial Sarcoma Tuesday, May 17, 2016
P8 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
23
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
P463 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Progression from Respiratory Dysfunction to Failure in Late-Onset Pompe Disease
C45: Dyspnea: Takes Your Breath Away
Area D, Hall D (North Building, Lower Level), Moscone Center
P612 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
The Effect of Inhaled Hypertonic Saline on Quality of Life in Primary Ciliary Dyskinesia Patients: A Double-Blind Randomized Controlled Cross-Over Trial
A51: Bronchiectasis: Clinical And Epidemiologic Studies
Area F, Hall D (North Building, Lower Level), Moscone Center
P616 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Clinical Features and Associated Likelihood of Primary Ciliary Dyskinesia in Adults
A51: Bronchiectasis: Clinical And Epidemiologic Studies
Area F, Hall D (North Building, Lower Level), Moscone Center
P617 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Determinants of Respiratory Function in Adults Patients with Primary Ciliary Dyskinesia
A51: Bronchiectasis: Clinical And Epidemiologic Studies
Area F, Hall D (North Building, Lower Level), Moscone Center
9:00 am-11:00 am; Oral Presentation 9:00 am
Does Cardiopulmonary Fitness and Pulmonary Function Differ Between Age Matched Groups of Children with Primary Ciliary Dyskinesia (PCD) and Cystic Fibrosis (CF) During One Year?
B19: Best Of Pediatrics
Room 3006/3008 (West Building, Level 3), Moscone Center
P489 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Late Diagnosis of Primary Ciliary Dyskinesia in a Kuwaiti 38-Year-Old Male
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P581 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Probable Primary Ciliary Dyskinesia in the Presence of Complex Congenital Heart Disease and Juvenile Dermatomyositis
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
P593 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Primary Ciliary Dyskinesia, Hypotrichosis and Macular Dystrophy: Coincidence or a Novel Syndrome?
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
P966 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Deletion of Rsph1 in a Mouse Model of Primary Ciliary Dyskinesia Results in a Mild Phenotype
C74: Models And Methods In Lung Biology
Area H, Hall D (North Building, Lower Level), Moscone Center
9:00 am-11:00 am; Oral Presentation 9:00 am
Respiratory Microbiology in Primary Ciliary Dyskinesia: Comparisons to a Pediatric Cystic Fibrosis Cohort
D18: Cystic Fibrosis And Primary Ciliary Dyskinesia: Two Sides Of The Same Coin?
Room 3007/3009 (West Building, Level 3), Moscone Center
9:00 am-11:00 am; Oral Presentation 9:30 am
A Comparison of Anaerobic to Aerobic Power Ratio in Children with Primary Ciliary Dyskinesia and Healthy Controls
D18: Cystic Fibrosis And Primary Ciliary Dyskinesia: Two Sides Of The Same Coin?
Room 3007/3009 (West Building, Level 3), Moscone Center
Pompe Disease Tuesday, May 17, 2016
Primary Ciliary Dyskinesia (PCD) Sunday, May 15, 2016
Monday, May 16, 2016
Tuesday, May 17, 2016
Wednesday, May 18, 2016
24
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Wednesday, May 18, 2016
P524 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
HEATR2 Regulates Ciliogenesis and Distinguishes Subclasses of Preassembly Factors Mutated in Primary Ciliary Dyskinesia
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P525 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Cri-du-Chat Syndrome and Primary Ciliary Dyskinesia: A Genetic and Clinical Connection
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P526 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Toronto Database Registry Pilot Cohort Study: Effect of Proximity to a PCD Center and Drug Insurance Coverage on Health Outcomes
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P527 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Development and Treatment of Chronic Rhinosinusitis in a Mouse Model of Primary Ciliary Dyskinesia
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P528 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Nup153 Gene Mutation Leads to Heterotaxy Through Defective SMAD1/ BMP Signaling
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P539 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Natural Evolution and Impact of Respiratory Tract Infections in Nasal Nitric Oxide Level During First 2 Years of Life - A Longitudinal Study
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P540 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Nasal Nitric Oxide in Primary Immunodeficiency: Helping to Distinguish Between Clinically Similar Diseases
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P542 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Ciliary Functional Biomarker Analysis in Pediatric Patients with Chronic Cough
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P543 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Mannose Binding Lectin and Its Impact on Patients with Primary Ciliary Dyskinesia
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
P556 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Tracheobronchomegaly (Mounier-Kuhn) and Primary Ciliary Dyskinesia
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
A Case of Primary Pulmonary Amoebiasis
D49: Lung Infection Case Reports II: Infections Other Than Fungal Infections
Area G, Hall D (North Building, Lower Level), Moscone Center
Clinical Characteristics and Treatment Outcomes of Primary Pulmonary Artery Sarcoma in Korea
D54: Clinical Pulmonary Hypertension
Area H, Hall D (North Building, Lower Level), Moscone Center
Primary Pulmonary Amoebiasis Wednesday, May 18, 2016
P847 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Primary Pulmonary Artery Sarcoma Wednesday, May 18, 2016
P1020 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
25
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
A Rare Case of Primary Pulmonary Melanoma
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Primary Pulmonary Synovial Sarcoma- A Rare Aggressive Tumor and a Diagnostic Challenge
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Function Tests in a 2-Year-Old Male with Prune-Belly Syndrome and Renal Failure Undergoing Peritoneal Dialysis
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Hypertension Due to Unilateral Pulmonary Agenesis
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
101 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Increased Concentration of BAFF and APRIL in Patients with Autoimmune Pulmonary Alveolar Proteinosis
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
110 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Clinical Information of Secondary Pulmonary Alveolar Proteinosis in Japan: A Follow-Up Report (KAKEN26305028/AMED:H27-063)
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
116 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Whole Lung Lavage Therapy of Pulmonary Alveolar Proteinosis: A Global Survey of Current Practices and Procedures
A24: Autoimmune Interstitial Lung Disease
Room 133 (North Building, Lower Level), Moscone Center
P698 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rare Association of Anti-Threonyl tRNA (PL-7) Antisynthetase Syndrome and Pulmonary Alveolar Proteinosis
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P704 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Mycobacterium Avium Complex Secondary to Pulmonary Alveolar Proteinosis: A Case Report
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
P1238 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Hepatic Steatosis Accompanies Pulmonary Alveolar Proteinosis
A42: Autoimmune Myositis, Antisynthetase, Scleroderma, And IPAF
Area L, Hall D (North Building, Lower Level), Moscone Center
Primary Pulmonary Melanoma Wednesday, May 18, 2016
322 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Primary Pulmonary Synovial Sarcoma Tuesday, May 17, 2016
P59 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Prune-Belly Syndrome (Eagle-Barrett Syndrome) Tuesday, May 17, 2016
P571 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Agenesis Monday, May 16, 2016
P63 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Alveolar Proteinosis (PAP) Sunday, May 15, 2016
26
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P1340 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Progressive Dyspnea in a Heart Transplant Recipient: Sirolimus-Induced Pulmonary Alveolar Proteinosis
A48: Conventional Drug Associated Lung Disease
Area L, Hall D (North Building, Lower Level), Moscone Center
P439 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Estimation of the True GM-CSF Autoantibody Concentration in the Sera of Healthy Subjects
A73: Lung Fibrosis: New Directions To Inform The Future
Area D, Hall D (North Building, Lower Level), Moscone Center
P147 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Autoantibody Against GM-CSF Presented by MHC Class II in Autoimmune Pulmonary Alveolar Proteinosis
B32: Alveolar Macrophage Biology
Area B, Hall D (North Building, Lower Level), Moscone Center
P371 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Utility of Therapeutic Lobar Lung Lavage in Four Patients of Pulmonary Alveolar Proteinosis
B37: Interventional Pulmonary Medicine: Cool Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P684 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Efficacy of Pulmonary Macrophage Transplantation (PMT) Therapy Is Mediated by Mature Macrophages Without Requirement of Myeloid Progenitor Expansion
B52: Neonatal Lung Disease: From Bench To Babies
Area F, Hall D (North Building, Lower Level), Moscone Center
P1420 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Light Chain Genotype Analysis of GM-CSF Autoantibody in Autoimmune Pulmonary Alveolar Proteinosis by Next Generation Sequencing
B57: Fibrosis Biology
Area M, Hall D (North Building, Lower Level), Moscone Center
P1503 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Elderly-Onset Hereditary Pulmonary Alveolar Proteinosis and CSF2RA Mutation
B62: The Biology Of Scarring. Where Are We Now
Area M, Hall D (North Building, Lower Level), Moscone Center
P275 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Alveolar Proteinosis Co-Existing with Underlying Non Specific Interstitial Pneumonia
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P284 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pathological Findings of Removal Lungs from a Patient with Refractory Fibrotic Autoimune Pulmonary Alveolar Proteinosis After Bilateral Lung Transplantation
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P291 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Autoimmune Pulmonary Alveolar Proteinosis with Progressive Fibrosis Refractory to Treatment with Whole Lung Lavage, Inhaled Granulocyte Macrophage Colony-Stimulating Factor and Rituximab
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P292 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Acquired Pulmonary Alveolar Proteinosis Successfully Treated with Whole Lung Lavage
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P296 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Alveolar Proteinosis with Severe Hypoxemia: A Combined Therapeutic Strategy
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P298 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Autoimmune Pulmonary Alveolar Proteinosis with Fluctuating Disease Activity in Parallel with Tobacco Smoke Burden
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
Tuesday, May 17, 2016
27
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Tuesday, May 17, 2016
202 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Establishment of a National Registry for Pulmonary Alveolar Proteinosis in the United States
C102: Stategies To Understand ILD: Registries, Prognostic Indicators And More
Room 304 (South Building, Esplanade Level), Moscone Center
112 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Pulmonary Alveolar Proteinosis: A Case Series from a Reference Center in Brazil
C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Disease, And More
Room 133 (North Building, Lower Level), Moscone Center
9:00 am-11:00 am; Oral Presentation 10:30 am
Whole Lung Lavage Followed by Inhaled Sargramostim as Therapy of Autoimmune Pulmonary Alveolar Proteinosis
D15: New Therapies In ILD
Room 306/308 (South Building, Esplanade Level), Moscone Center
811 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Determining the Dose-Response Curve Needed to Translate Pulmonary Macrophage Transplantation (PMT) Therapy to Children with Hereditary Pulmonary Alveolar Proteinosis
D25: Neonatal Lung Diseases: From Bench To Babies
Room 3011 (West Building, Level 3), Moscone Center
506 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Pulmonary Alveolar Proteinosis Is Driven by Reduced GM-CSF-Dependent Cholesterol Clearance by Alveolar Macrophages, Not an Inability to Catabolize Surfactant Phospholipids
D27: Macrophages: Resolvers, Responders Or Both?
Room 2014 (West Building, Level 2), Moscone Center
P761 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Invasive Pulmonary Aspergillosis Revealed After Whole Lung Lavage for Pulmonary Alveolar Proteinosis
D48: Lung Infection Case Reports I: Fungal Infections
Area G, Hall D (North Building, Lower Level), Moscone Center
P513 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
A Panel of Novel Blood Tests Based on GM-CSF Signaling Facilitates the Differential Diagnosis of PAP-Causing Diseases
D50: Pediatric Rare Lung Diseases
Area E, Hall D (North Building, Lower Level), Moscone Center
510 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Pulmonary Alveolar Proteinosis Associated with Secondary Hemophagocytic Lymphohistiocytosis: A Pediatric Case of Whole Lung Lavage Under Veno-Venous Extracorporeal Membrane Oxygenation
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Wednesday, May 18, 2016
Pulmonary Arterial Hypertension, Idiopathic Sunday, May 15, 2016
907 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Whole Genome Sequencing in Idiopathic and Heritable Pulmonary Arterial Hypertension
A107: Etiology Of PAH: Go Your Own Way
Room 3014 (West Building, Level 3), Moscone Center
Monday, May 16, 2016
9:00 am-11:00 am; Oral Presentation 9:00 am
Utility of Deep Phenotyping in the Identification and Validation of Novel Causal Whole Genome Sequencing Variation in Patients with Pulmonary Arterial Hypertension
B20: Hooked On Ph’Omics
Room 3003/3005 (West Building, Level 3), Moscone Center
Pneumonectomy for the Management of Unilateral Pulmonary Artery Agenesis
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Artery Agenesis Monday, May 16, 2016
P79 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
28
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Idiopathic Pulmonary Artery Aneurysm
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Artery Sarcoma: The Retrospective Study of Clinical Presentation and Course
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Dangers of Flying High and Diving Low! An Unusual Case of Dyspnea
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Artery Aneurysm, Idiopathic Monday, May 16, 2016
P73 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Artery Sarcoma Tuesday, May 17, 2016
P57 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Bulla, Idiopathic Monday, May 16, 2016
P333 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Calcification Sunday, May 15, 2016
P1359 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Metastatic Pulmonary Calcification Following Orthotopic Liver Transplant: A Bronchoscopic Diagnosis
A48: Conventional Drug Associated Lung Disease
Area L, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P280 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Calcium: Great for Bones, Not for Lungs
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P288 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Alveolar Microlithiasis: A Case Report
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P301 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rare Case of Dendriform Pulmonary Ossification
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P303 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Osteogenesis Imperfecta Associated with Dendriform Pulmonary Ossification and Emphysematous Change
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P347 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Sandstorm Lung: A Case of Pulmonary Alveolar Microlithiasis
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P1422 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Revisiting Pulmonary Ossification
B57: Fibrosis Biology
Area M, Hall D (North Building, Lower Level), Moscone Center
P1517 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Low Phosphate Diet Arrests and Reverses Stone Accumulation and Acute Lung Injury in Mice with Pulmonary Alveolar Microlithiasis
C67: Acute Lung Injury
Area M, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
Tuesday, May 17, 2016
29
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Pulmonary Capillaritis Sunday, May 15, 2016
P700 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Idiopathic Pauci Immune Pulmonary Capillaritis (IPIPC)
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
503 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
A Case of Concomitant Diffuse Alveor Hemorrhage and Pulmonary Embolism in Idiopathic Pulmonary Capillaritis
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Multiple Calcified Pulmonary Nodules: Not Always Granulomatous!
B66: Lung Cancer Screening And Nodule Evaluation
Area E, Hall D (North Building, Lower Level), Moscone Center
Changes in Peripheral Airway Function with Pulmonary Graft Vs. Host Disease in a Longitudinal Study of Paediatric Bone Marrow Transplant Patients
C108: Advances In Lung Function Assessment
Room 2024 (West Building, Level 2), Moscone Center
P277 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Hyalinizing Granuloma: A Rare Pulmonary Cavitary Pseudotumor, a Case Report
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P278 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Hyalinising Granuloma with Sweet’s Syndrome
C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Severe BPD Complicated by PIG
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Leukemic Infiltration in the Setting of Acute Respiratory Failure
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
A Rare Case of a Primary Sarcoma of the Pulmonary Artery in a 56 Year Old Female: A Case Report
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Epithelioid Hemangioendothelioma Monday, May 16, 2016
P563 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Graft vs Host Disease Tuesday, May 17, 2016
611 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
Pulmonary Hyalinizing Granuloma Tuesday, May 17, 2016
Pulmonary Interstitial Glycogenosis Tuesday, May 17, 2016
P573 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Leukemic Infiltration Wednesday, May 18, 2016
313 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Pulmonary Sarcoma Monday, May 16, 2016
P57 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
30
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
P330 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Intra-Lobar Pulmonary Sequestration: A Unique and Potentially Fatal Cause of Hemoptysis
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P348 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Pulmonary Sequestration Presenting with Post Prandial Epigastric Pain
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
When Ventilation-Perfusion Scan Falters: A Rare Cause of Chronic Pleuritic Chest Pain, Hypoxia, and Pulmonary Hypertension
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Vein Varix: A Rare Incidental Finding
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Sequestration Monday, May 16, 2016
Pulmonary Vein Stenosis Monday, May 16, 2016
P61 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Vein Varix Monday, May 16, 2016
P60 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pulmonary Veno-Occlusive Disease (PVOD) Monday, May 16, 2016
P66 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Atypical Hemolytic Uremic Syndrome (HUS) and Pulmonary Veno-Occlusive Disease (PVOD)
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
1017 2:15 pm-4:15 pm; Poster Viewing 2:15-3:00 pm; Poster Discussion 3:00-4:15 pm
EIF2AK4 Mutation-Carriers with PVOD Present Distinct Features Within the Remodeled Lung Vasculature
C106: Wrecking Ball: New Paradigms In Understanding And Treatment Of PH
Room 3024 (West Building, Level 3), Moscone Center
An Incidental Pulmonary Vein Thrombosis - Resolution with Watchful Waiting
B54: Case Reports In The Pulmonary Circulation
Area A, Hall D (North Building, Lower Level), Moscone Center
Recurrent Respiratory Papillomatosis Involving the Lower Airways Treated with Argon Plasma Coagulation and Cidofovir Intralesional Injection
B39: Interventional Pulmonary Medicine: Recent Advances
Area D, Hall D (North Building, Lower Level), Moscone Center
Pulmonary Venous Thrombosis Monday, May 16, 2016
P76 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Recurrent Respiratory Papillomatosis Monday, May 16, 2016
P464 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Relapsing Polychondritis Sunday, May 15, 2016
P1602 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Reassess the Value of 18F-FDG PET/CT for Relapsing Polychondritis Diagnose and Therapeutic Response Monitoring
A79: Lung Imaging: CT And Beyond
Area N, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P450 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Quantitative CT Measurement of Tracheal Cross-Sectional Areas in Relapsing Polychondritis: Correlations with Spirometric Values
B39: Interventional Pulmonary Medicine: Recent Advances
Area D, Hall D (North Building, Lower Level), Moscone Center
31
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Monday, May 16, 2016
P470 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rheumatologic Disorder Mimicking Asthma
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
524 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Presentation of Relapsing Polychondritis in an Adolescent
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Congenital Pulmonary Artery Atresia Masquerading as a Left Sided Anomaly
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
Successful Management of Breathing-Related Sleep Disorder Associated with an Orphan Syndrome, Rapid-Onset Obesity with Hypothalamic Dysfunction, Hypoventilation, and Autonomic Dysregulation (ROHHAD)
B65: Things That Go Bump In The Night: Sleep Case Studies And Non-OSA Sleep
Area N, Hall D (North Building, Lower Level), Moscone Center
P692 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
37 Year Old Female with 7 Year History of Intermittent Dyspnea of Few Minutes Duration
A35: Case Reports In Autoimmune Lung Disease
Area G, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P140 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Overview of Multicenter Genomic Research in Alpha-1 Antitrypsin Deficiency and Sarcoidosis (GRADS) and Biorepository
B31: Alpha-1 Antitrypsin Deficiency
Area B, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P240 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Resolution of Cardiac Magnetic Resonance T2 Signal Following Immune Suppression for Cardiac Sarcoidosis: A Case Series
C40: Sarcoidosis: Understanding This Multi-System Disorder
Area C, Hall D (North Building, Lower Level), Moscone Center
P319 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Sarcoidosis and Sjogren’s Syndrome: Clues Suggesting Overlap Rather than Mimicry
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P116 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Pathologic Rarity
C81: Unusual Presentations Of Lung Cancer: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
P129 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Case of Sarcomatoid Carcinoma of the Lung in a Young Female
C81: Unusual Presentations Of Lung Cancer: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Right Pulmonary Artery Atresia Wednesday, May 18, 2016
505 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
ROHHAD Syndrome Monday, May 16, 2016
P1577 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Rosai Dorfman Disease Sunday, May 15, 2016 Sarcoidosis
Sarcomatoid Carcinoma Tuesday, May 17, 2016
32
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Scimitar Syndrome Presenting with Pulmonary Emboli and Right Heart Failure Requiring ECMO
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
An “Ancient” Cause of an Anterior Mediastinal Mass
B40: Dyspnea: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Short Telomere Syndrome a Rare Cause of Familial Idiopathic Pulmonary Fibrosis
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P1333 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Shrinking Lung Syndrome - An Unusual Cause of Dyspnea in Patients with Systemic Lupus Erythematosus
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
P1334 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Dyspnea in Systemic Lupus Erythematosus: A Case of Shrinking Lung Syndrome
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
An Infant with Tachypnea and Progressive Respiratory Failure
D108: Pediatric Cases: A Room Full Of Zebras
Room 2014 (West Building, Level 2), Moscone Center
A Case of Sarcoidosis and Sjogren’s Syndrome: Clues Suggesting Overlap Rather than Mimicry
C44: Diffuse Parenchymal Lung Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Endobronchial Ultrasound Bronchoscopy in the Diagnosis of Mediastinal Solitary Fibrous Tumor
B37: Interventional Pulmonary Medicine: Cool Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Expression of the Surfactant Protein C Mutant SP-CI73T in Mice Results in Dose Dependent Disruption of Lung Development and Age Related Diffuse Parenchymal Lung Remodeling In Adults
C17: Fascinating Mechanisms In Lung Fibrosis
Room 2020/2022 (West Building, Level 2), Moscone Center
Scimitar Syndrome Sunday, May 15, 2016
P1463 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Sclerosing Thymoma Monday, May 16, 2016
P362 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Short Telomere Syndrome and Idiopathic Pulmonary Fibrosis Tuesday, May 17, 2016
P311 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Shrinking Lung Syndrome Sunday, May 15, 2016
Shwachman-Diamond Syndrome Wednesday, May 18, 2016
521 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
Sjogren’s Overlap Syndrome Tuesday, May 17, 2016
P319 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Solitary Fibrous Tumor Monday, May 16, 2016
P377 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
SP-C Related Interstitial Lung Disease Tuesday, May 17, 2016
9:00 am-11:00 am; Oral Presentation 9:15 am
33
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Appearances Are Deceptive: An Unusual Presentation of a Rare Primary Lung Tumor!!
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Spindle Cell Carcinoma Tuesday, May 17, 2016
P84 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Surfactant Protein-Associated Lung Disease Monday, May 16, 2016
P1538 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
SFTPA1 Mutation in Familial Idiopathic Interstitial Pneumonia and Lung Cancer
B62: The Biology Of Scarring. Where Are We Now
Area M, Hall D (North Building, Lower Level), Moscone Center
Tuesday, May 17, 2016
P596 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Successful Outcome of a Genetic Lethal Condition in a Term Newborn
C62: Pediatric Cases I
Area E, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
815 9:00 am-11:00 am; Poster Viewing 9:00-9:45 am; Poster Discussion 9:45-11:00 am
Multiplexed Direct Genomic Selection Identifies Exonic, Intronic, and Copy Number Variation in Surfactant-Associated Genes Among Infants with Respiratory Distress Syndrome (RDS) and Children with Interstitial Lung Disease (chILD)
D25: Neonatal Lung Diseases: From Bench To Babies
Room 3011 (West Building, Level 3), Moscone Center
An Atypical Presentation of Acute Febrile Neutrophilic Dermatosis as Drug-Induced Bullous Variant Sweet’s Syndrome
C53: Critical Care Case Reports: Multisystem Organ Failure
Area G, Hall D (North Building, Lower Level), Moscone Center
Sweet’s Syndrome Tuesday, May 17, 2016
P856 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Swyer-James Syndrome Sunday, May 15, 2016
P1446 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Unusual Clinical Presentation for Swyer-James-Macleod Syndrome
A67: Case Reports In Pulmonary Vascular Disease
Area M, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P487 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Swyer-James-MacLeod Syndrome Misdiagnosed as COPD
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P491 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
New Diagnosis of Swyer-James-Macleod Syndrome in An Adult: A Case Report
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
P578 9:00 am-3:30 pm; Poster Viewing 11:00 am-12:45 pm
Unilateral Hyperlucent Lung in an Infant
D51: Pediatric Cases II
Area E, Hall D (North Building, Lower Level), Moscone Center
P293 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Malignancy Mimic: An Unexpected Consequence of an Abdominal Gun Shot Wound
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
P294 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Pleural Noduarity in a Vietnam Veteran
B38: Pleural Disease: Case Reports
Area C, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
Thoracic Splenosis Monday, May 16, 2016
34
Rare Disease Term Date/Day
Board Number/Time
Abstract Title
Session ID and Title
Location
Sunday, May 15, 2016
P1322 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Flash Blood - An Unusual Case of Intermittent Massive Hemoptysis
A47: Rare Interstitial Lung Disease: Case Reports
Area L, Hall D (North Building, Lower Level), Moscone Center
Monday, May 16, 2016
P475 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Tracheobronchial-Esophageal Fistula in a 23 Year Old with “Asthma”
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Tracheal Fistula
Tracheal Hamartoma Tuesday, May 17, 2016
P76 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
A Rare Case of Tracheal Hamartoma
C80: Thoracic Oncology: Case Reports
Area A, Hall D (North Building, Lower Level), Moscone Center
Wednesday, May 18, 2016
323 1:30 pm-3:30 pm; Poster Viewing 1:30-2:15 pm; Poster Discussion 2:15-3:30 pm
An Asymptomatic Case of Tracheal Hamartoma
D110: Unusual Tumors Of The Chest
Room 309 (South Building, Esplanade Level), Moscone Center
Exercise Induced Respiratory Insufficiency in a Murine Model of Very Long-Chain Acyl-CoA Dehydrogenase Deficiency
C75: Improving And Assessing Respiratory Function
Area H, Hall D (North Building, Lower Level), Moscone Center
Yellow Nail Syndrome
B45: Obstructive Lung Disease: Interesting Cases
Area D, Hall D (North Building, Lower Level), Moscone Center
Very Long-Chain Acyl-CoA Dehydrogenase Deficiency Tuesday, May 17, 2016
P983 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
Yellow Nail Syndrome Monday, May 16, 2016
P488 9:00 am-4:15 pm; Poster Viewing 11:00 am-12:45 pm
35
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Sunday, May 15, 2016 6:30 pm - 9:30 pm Marriott Marquis, San Francisco Golden Gate B ADMISSION IS COMPLIMENTARY AND WILL BE ON A FIRST-COME, FIRST-SERVED BASIS. DINNER WILL BE PROVIDED. An Industry-Organized Symposium at the ATS 2016 International Conference. All ATS 2016 International Conference attendees are invited to this non-CME/CNE educational program sponsored by Boehringer Ingelheim Pharmaceuticals, Inc. Attendance is limited to healthcare professionals only. Aspects of this program may be reportable under the physician payments Sunshine Act. CME, continuing medical education; CNE, continuing nursing education.
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