Brain & Development 23 (2001) 824–831 www.elsevier.com/locate/braindev

Cumulative Contents to Volume 23 Vol. 23, No. 1 Editor-in-Chief’s Address Y. Suzuki

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Review article Malformations of cortical development and epilepsy R.I. Kuzniecky, A.J. Barkovich (USA)

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Original articles Epilepsy associated with infantile hemiparesis: predictors of long-term evolution R. Gaggero, R. Devescovi, A. Zaccone, G. Ravera (Italy) Pseudo-TORCH syndrome or Baraitser–Reardon syndrome: diagnostic criteria R. Vivarelli, S. Grosso, M. Cioni, P. Galluzzi, L. Monti, G. Morgese, P. Balestri (Italy) CSF glutamate/GABA concentrations in pyridoxine-dependent seizures: etiology of pyridoxine-dependent seizures and the mechanisms of pyridoxine action in seizure control T. Goto, N. Matsuo, T. Takahashi (Japan) The clinical course of childhood and adolescent adrenoleukodystrophy before and after Lorenzo’s oil Y. Suzuki, A. Imamura, N. Shimozawa, N. Kondo (Japan) Gait patterns in children with spastic diplegia and periventricular leukomalacia K. Yokochi (Japan) Benign paroxysmal vertigo of childhood P. Drigo, G. Carli, A.M. Laverda (Italy) The spectrum of postinfectious encephalomyelitis K.-L. Hung, H.-T. Liao, M.-L. Tsai (Taiwan, ROC) Magnetic resonance imaging in diplegic form of cerebral palsy Z. Seidl, J. Su¨ssova´, J.V. Obenberger, M. Vaneˇc`kova´, T. Vita´k, J. Rydland (Czech Republic, Norway) Bax-induced apoptosis not demonstrated in the congenital toxoplasmosis in mice J. Takahashi, T. Fukuda, J. Tanaka, M. Minamitani, K. Onouchi, A. Makioka (Japan) Case reports Varicella-associated acute necrotizing encephalopathy with a good prognosis T.D. Tran, M. Kubota, K. Takeshita, M. Yanagisawa, Y. Sakakihara (Japan) A Japanese girl with leukoencephalopathy with vanishing white matter C. Sugiura, H. Miyata, A. Oka, S. Takashima, E. Ohama, K. Takeshita (Japan) Forced normalization induced by ethosuximide therapy in a patient with intractable myoclonic epilepsy T. Yamamoto, J.R. Pipo, S. Akaboshi, S. Narai (Japan)

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24 30 34 38 42 46 50

54 58 62

Bibliography in child neurology Bibliography of congenital muscular dystrophies – cobblestone lissencephalies: Series III (1999) Y. Fukuyama (Japan)

65

Letter to the Editor Phenytoin administration in the newborn and infant D. Neubauer, M. Novosel-Sever (Slovenia)

75

Meeting reports The 30th Annual Meeting Of The Chugoku-Shikoku Study Group On Infantile Spasms And Allied Disorders, 25 March 2000 (Okayama, Japan) E. Oka (Japan) The 17th annual conference on neuromuscular diseases in childhood

76 77

Announcements and reports

79

Cumulative Contents to Volume 23 Instructions to authors Congress announcement

825 81 I

Vol. 23, No. 2 Review article Mutism: elective or selective, and acquired N. Gordon (UK) Original articles Neurocognitive development of children with congenital unilateral brain lesion and epilepsy A. Kolk, A. Beilmann, T. Tomberg, A. Napa, T. Talvik (Estonia) Clinicopathological study on eyes from cases of Fukuyama type congenital muscular dystrophy N. Hino, M. Kobayashi, N. Shibata, T. Yamamoto, K. Saito, M. Osawa (Japan) Ataxia and Congenital Muscular Dystrophy: the follow-up of a new specific phenotype C.P. Trevisan, E. Pastorello, S. Tonello, M. Armani, M.T. Rigoni, A.P. Tormene, M.P. Freda, M. Zortea, S. Lombardi (Italy) Electroencephalographic changes and their regional differences during pediatric cardiovascular surgery with hypothermia T. Akiyama, K. Kobayashi, T. Nakahori, H. Yoshinaga, T. Ogino, Y. Ohtsuka, M. Takeuchi, K. Morita, S. Sano, E. Oka (Japan) Case reports Occlusive hydrocephalus in congenital myotonic dystrophy W. Rettwitz-Volk, M. Wikstroem, O. Flodmark (Germany, Sweden) Papillitis as an onset sign of Leber’s hereditary optic neuropathy: a case report C. Pantaleoni, S. D’Arrigo, I. Bagnasco, E. Piozzi, F. Carrara, V. Scaioli, D. Riva (Italy) The first case of 4-hydroxybutyric aciduria in Japan Y. Ishiguro, M. Kajita, T. Aoshima, K. Watanabe, M. Kimura, S. Yamaguchi (Japan) A variant case of congenital bilateral perisylvian syndrome with asymmetric findings on neuroimaging and septum pellucidum defect H. Sejima, Y. Takusa, M. Kimura, Y. Tamaoki, K. Kishi, S. Yamaguchi (Japan) Alleviation of sleep disturbance and repetitive behavior by a selective serotonin re-uptake inhibitor in a boy with Asperger’s syndrome J. Furusho, K. Matsuzaki, I. Ichihashi, H. Satoh, K. Yamaguchi, K. Kumagai (Japan)

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88 97 108 115

122 125 128 131 135

Announcements and Reports

138

Instructions to Authors

140

Announcement

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Congress announcement

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Vol. 23, No. 3 Aetiology and Epidemiology (ETI)

145

Animal models (ANM)

152

Clinical diagnostic (CDG)

153

Neuroinstrumental diagnostic (NDG)

157

Additional handicaps (ADH)

162

Therapy (THE)

165

Strategies of evaluation (SEV)

181

Outcome (OUT)

185

Sport and Recreation (SPR)

188

Miscellaneous (MIS) 191 Author Index

192

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Announcements and Reports

194

Instruction to Authors

196

Congress announcement

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Vol. 23, No. 4 Review article Surgical treatment of medically refractory epilepsy in childhood O.C. Snead (Canada)

199

Guidelines Guidelines for reporting clinical features in cases with MECP2 mutations A.M. Kerr, Y. Nomura, D. Armstrong, M. Anvret, P.V. Belichenko, S. Budden, H. Cass, J. Christodoulou, A. Clarke, C. Ellaway, M. d’Esposito, U. Francke, M. Hulten, P. Julu, H. Leonard, S. Naidu, C. Schanen, T. Webb, I.W. Engerstrom, Y. Yamashita, M. Segawa (UK, Japan, USA, Sweden, Russia, Australia)

208

Original articles Mutational analysis of MECP2 in Japanese patients with atypical Rett syndrome K. Inui, M. Akagi, J. Ono, H. Tsukamoto, K. Shimono, T. Mano, K. Imai, M. Yamada, T. Muramatsu, N. Sakai, S. Okada (Japan) Unilateral polymicrogyria: a common cause of hemiplegia of prenatal origin I. Pascual-Castroviejo, S.I. Pascual-Pascual, J. Vian˜ o, V. Martinez, R. Palencia (Spain) The role of Glial–Pial barrier lesions and impaired vascularization in anomalous formation of cortical convolutions M. Da˛ mbska, M. Laure-Kamionowska (Poland) Etiologic determination of childhood developmental delay M.I. Shevell, A. Majnemer, P. Rosenbaum, M. Abrahamowicz (Canada) Case reports Four siblings with Hallervorden–Spatz disease U. Vaher, A. Napa, A. Nurmiste, A. Piirsoo, H. Sibul, T. Talvik (Estonia) Lamotrigine in two cases of Rett syndrome ¨ ztu¨ rk, H. Per (Turkey) S. Kumandas, H. C¸ aksen, A. C ¸ iftc¸ i, M. O A severely brain-damaged case of 3-hydroxyisobutyric aciduria M. Sasaki, H. Iwata, K. Sugai, M. Fukumizu, M. Kimura, S. Yamaguchi (Japan) Acquired epileptiform opercular syndrome: a case report and results of single photon emission computed tomography and computer-assisted electroencephalographic analysis E. Tachikawa, H. Oguni, S. Shirakawa, M. Funatsuka, K. Hayashi, M. Osawa (Japan) A 10-year-old boy with Marfan syndrome exhibiting cerebrovascular abnormalities M. Kondo, S. Itoh, K. Nagano, M. Namba, M. Kondo, T. Imai, S. Onishi (Japan) L-2-Hydroxyglutaric aciduria presenting as status epilepticus D.I. Zafeiriou, A. Sewell, P. Savvopoulou-Augoustidou, N. Gombakis, G. Katzos (Greece, Germany) Inflammatory pathological changes in a 2-year-old boy with Charcot–Marie–Tooth disease Y. Nakai, A. Okumura, H. Takada, T. Negoro, K. Watanabe, N. Hattori, G. Sobue (Japan) Transient cheiro-oral syndrome due to a ruptured intracranial dermoid cyst M. Nakamura, M. Mizuguchi, M.Y. Momoi, H. Chou, T. Masuzawa (Japan) Epileptic seizures and structural abnormalities in a patient with holoprosencephaly S. Takahashi, Y. Takahashi, N. Kondo, T. Orii (Japan)

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246 251 255 258 261 264

Letter to the Editor Guidelines for reporting clinical features in cases with MECP2 mutations, by Alison Kerr and an international group M. Segawa (Japan)

269

Erratum Erratum to ‘‘Bradev 22, No. 7 Table of Contents’’

270

Announcements and reports

271

Instructions to authors

273

Congress announcement

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Cumulative Contents to Volume 23

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Vol. 23, No. 5 Review article Newer antiepileptic drugs: advantages and disadvantages S.J. Wallace (UK)

277

Communication Galactonojirimycin derivatives restore mutant human b-galactosidase activities expressed in fibroblasts from enzyme-deficient knockout mouse L. Tominaga, Y. Ogawa, M. Taniguchi, K. Ohno, J. Matsuda, A. Oshima, Y. Suzuki, E. Nanba (Japan)

284

Original articles Progressive neuronal loss in the ventral posterior lateral and medial nuclei of thalamus in Niemann–Pick disease type C mouse brain A. Yamada, M. Saji, Y. Ukita, Y. Shinoda, M. Taniguchi, K. Higaki, H. Ninomiya, K. Ohno (Japan) The significance of type 1 fiber atrophy (hypotrophy) in childhood neuromuscular disorders C. Imoto, I. Nonaka (Japan) Long-term effect of flunarizine on patients with alternating hemiplegia of childhood in Japan M. Sasaki, N. Sakuragawa, M. Osawa (Japan) Clinical and EEG findings in 18 cases of late infantile neuronal ceroid lipofuscinosis E. Veneselli, R. Biancheri, S. Buoni, A. Fois (Italy) A functional magnetic resonance imaging study during sentence reading in Japanese dyslexic children A. Seki, T. Koeda, S. Sugihara, M. Kamba, Y. Hirata, T. Ogawa, K. Takeshita (Japan) Prevalence of positive anticardiolipin antibody in benign infantile convulsion K. Yoshimura, T. Konishi, H. Kotani, H. Wakiguchi, T. Kurashige (Japan) The gene copy ratios of SMN1/SMN2 in Japanese carriers with type I spinal muscular atrophy T. Diep Tran, T. Kroepfl, M. Saito, M. Nagura, H. Ichiseki, M. Kubota, T. Toda, Y. Sakakihara (Japan, Austria) Motor functions in non-ambulatory children with spastic diplegia and periventricular leukomalacia K. Yokochi (Japan) The variety of visual perceptual impairments in pre-school children with perinatal brain damage P. Stiers, B.M. van den Hout, M. Haers, R. Vanderkelen, L.S. de Vries, O. van Nieuwenhuizen, E. Vandenbussche (Belgium, The Netherlands) Prolonged suppression of brain nitric oxide synthase activity by 7-nitroindazole protects against cerebral hypoxic–ischemic injury in neonatal rat A. Ishida, W.H. Trescher, M.S. Lange, M.V. Johnston (USA)

288 298 303 306 312 317 321 327 333 349

Case reports Encephalocraniocutaneous lipomatosis associated with iris coloboma, chorioretinitis and spinal cord involvement: a case report G. Deda, H. C¸ aksen, G. Yavuzer, T. Arasıl (Turkey) Early infantile epileptic encephalopathy (Ohtahara syndrome) after maternal electric injury during pregnancy: etiological considerations T. Krasemann, S. Hoovey, J. Uekoetter, H. Bosse, G. Kurlemann, O.M. Debus (Germany)

359

Book reviews

363

Letter to the Editor Acute striatal necrosis following measles in children K.A. Voudris, A. Skardoutsou, E.A. Vagiakou (Greece)

365

Announcements and reports

366

Instructions to authors

367

Announcement

370

Congress announcement

355

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Vol. 23, No. 6 Origional articles Joint deformity patterns in severely physically disabled patients K. Yokochi (Japan) Seizure frequency and characteristics in children with Down syndrome H. Goldberg-Stern, R.H. Strawsburg, B. Patterson, F. Hickey, M. Bare, N. Gadoth, T.J. Degrauw (Israel, USA) Development of lysosomal storage in mice with targeted disruption of the b-galactosidase gene: a model of human GM1-gangliosidosis M. Itoh, J. Matsuda, O. Suzuki, A. Ogura, A. Oshima, T. Tai, Y. Suzuki, S. Takashima (Japan) Serial magnetic resonance imaging findings in mucopolysaccharidosis IIIB (Sanfilippo’s syndrome B) D.I. Zafeiriou, P.A. Savvopoulou-Augoustidou, A. Sewell, F. Papadopoulou, M. Badouraki, E. Vargiami, N.P. Gombakis, G.S. Katzos (Greece, Germany)

371 375 379

385

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Cumulative Contents to Volume 23

Relation between the date of cyst formation observable on ultrasonography and the timing of injury determined by serial electroencephalography in preterm infants with periventricular leukomalacia T. Kubota, A. Okumura, F. Hayakawa, T. Kato, K. Itomi, K. Kuno, K. Watanabe (Japan) Body position-dependent changes in cerebral hemodynamics during apnea in preterm infants G. Pichler, G. Schmo¨ lzer, W. Mu¨ ller, B. Urlesberger (Austria) Clinical and electroencephalographic findings in early and late onset benign childhood epilepsy with occipital paroxysms M.-L. Tsai, H.-Y. Lo, W.-T. Chaou (Taiwan) Different effects between 7-nitroindazole and l-NAME on cerebral hemodynamics and hippocampal lesions during kainic acid-induced seizures in newborn rabbits Y. Takei, S. Takashima, J. Ohyu, K. Matsuura, N. Katoh, T. Takami, T. Miyajima, A. Hoshika (Japan) Sites and temporal changes of gangliosides GM1/GM2 storage in the Niemann–Pick disease type C mouse brain M. Taniguchi, Y. Shinoda, H. Ninomiya, M.T. Vanier, K. Ohno (Japan, France) Empty sella in children as a key for diagnosis J.-i. Takanashi, H. Suzuki, K. Nagasawa, K. Kobayashi, N. Saeki, Y. Kohno (Japan)

390 395 401

406 414 422

Case reports Plasmapheresis in fulminant acute disseminated encephalomyelitis R. Miyazawa, A. Hikima, Y. Takano, H. Arakawa, T. Tomomasa, A. Morikawa (Japan) A case of early-onset benign occipital seizure susceptibility syndrome: decreased cerebral blood flow in the occipital region detected by interictal single photon emission computed tomography, corresponding to the epileptogenic focus M. Sakagami, Y. Takahashi, H. Matsuoka, T. Hoshida, K. Izaki, S. Nouka, A. Yoshioka (Japan)

427

Meeting report

431

Book review

432

Announcements and reports

433

Instructions to authors

434

Announcements

437

Congress announcement

424

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Vol. 23, No. 7 Preface Y. Fukuyama A special note on terminology of West syndrome and infantile spasms Y. Fukuyama (Japan) West & son: the origins of West syndrome A.L. Lux (UK) Perspectives and Clinico-Electrical Delineation of West Syndrome What is West syndrome? O. Dulac (France) Symptomatology of infantile spasms K. Watanabe, T. Negoro, A. Okumura (Japan) Neurophysiology of spasms F. Vigevano, L. Fusco, C. Pachatz (Italy) Spasms in clusters in epilepsies other than typical West syndrome Y. Ohtsuka, K. Kobayashi, T. Ogino, E. Oka (Japan) Clinico-electrical evolution in pre-hypsarrhythmic stage: towards prediction and prevention of West syndrome A. Okumura, K. Watanabe (Japan) Neurobiological Substrates of West Syndrome Neuroradiological assessment of brain structure and function and its implication in the pathogenesis of West syndrome C. Juha´ sz, H.T. Chugani, O. Muzik, D.C. Chugani (USA) Mechanism of tonic spasms in West syndrome viewed from ictal SPECT findings K. Haginoya, M. Munakata, H. Yokoyama, R. Kato, S. Tanaka, M. Hirose, M. Ishitobi, K. Kon, Y. Yoshihara, M. Takayanagi, T. Yamazaki, K. Iinuma (Japan) Infantile spasms in tuberous sclerosis complex P. Curatolo, S. Seri, M. Verdecchia, R. Bombardieri (Italy)

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447 453 467 473 482

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496 502

Cumulative Contents to Volume 23 Neuropathology of tuberous sclerosis M. Mizuguchi, S. Takashima (Japan) Neuropathology of the limbic system and brainstem in West syndrome M. Hayashi (Japan) Polysomnographical assessment of the pathophysiology of West syndrome J. Kohyama (Japan) Magnetoencephalography in the detection of focal lesions in West syndrome H. Hattori, T. Yamano, T. Tsutada, N. Tsuyuguchi, H. Kawawaki, M. Shimogawara (Japan) Pathogenesis and Epidemiology of West Syndrome How do the many etiologies of West syndrome lead to excitability and seizures? The corticotropin releasing hormone excess hypothesis K.L. Brunson, M. Eghbal-Ahmadi, T.Z. Baram (USA) Epidemiological data of West syndrome in Finland R. Riikonen (Finland) The role of central histaminergic neuron system as an anticonvulsive mechanism in developing brain H. Yokoyama (Japan) Serum cytokine levels are altered in patients with West syndrome Z.-S. Liu, Q.-W. Wang, F.-L. Wang, L.-Z. Yang (People’s Republic of China) Clinical analysis of West syndrome associated with phenylketonuria Z. Zhongshu, Y. Weiming, F. Yukio, Z. Cheng-(L)Ning, W. Zhixing (People’s Republic of China, Japan) Clinical and pedigree study on familial cases of West syndrome in Japan K. Sugai, Y. Fukuyama, K. Yasuda, S. Fujimoto, M. Ohtsu, H. Ohta, A. Ogawa, S.-i. Hamano, S. Hirano, H. Yoshioka, A. Ishikawa, T. Seki, N. Itokazu, R. Tawa (Japan) West Syndrome – Epidemiology and Current Status in Asia National survey on West syndrome in Korea Y.S. Hwang (South Korea) National survey of West syndrome in Taiwan C. Young (Taiwan) Epidemiological and clinical studies of West syndrome in Nagasaki Prefecture, Japan A. Matsuo, T. Matsuzaka, A. Tsuru, H. Moriuchi, Y. Nakashita, S. Tanaka, C. Baba, K. Tomimasu (Japan) A population-based neuroepidemiological survey of West syndrome in Okayama Prefecture, Japan E. Oka, N. Murakami, I. Ohmori, T. Ogino (Japan) Epidemiology of West syndrome in Singapore W.-L. Lee, H.-T. Ong (Singapore) West syndrome: a university hospital based study from Oman R. Koul, A. Chacko, E. Cherian (Oman) West syndrome and other infantile epileptic encephalopathies – Indian hospital experience V. Kalra, S. Gulati, R.M. Pandey, S. Menon (India) Early epileptic encephalopathies including West syndrome: a 3-year retrospective study from Klang Hospital, Malaysia M. Thambyayah (Malaysia) West syndrome in Thailand: a hospital-based survey S. Chiemchanya, A. Visudtibhan, P. Visudhiphan (Thailand) West syndrome – The University of Hong Kong experience (1970–2000) V. Wong (Hong Kong) West syndrome: the Philippine experience A.M. Salonga, M.B. Lukban, M.H. Ortiz, B. Balatero-Terencio, A.M. Lagman (Philippines) Updates in Therapies of West Syndrome The treatment of West syndrome: a Cochrane review of the literature to December 2000 E. Hancock, J.P. Osborne, P. Milner (UK) Extremely low-dose ACTH therapy for West syndrome in Japan M. Ito (Japan) ACTH therapy of West syndrome: Finnish views R. Riikonen (Finland) What are the reasons for the strikingly different approaches to the use of ACTH in infants with West syndrome? T.Z. Baram (USA) Vigabatrin for tuberous sclerosis complex P. Curatolo, M. Verdecchia, R. Bombardieri (Italy) High-dose vitamin B6 treatment in West syndrome Y. Toribe (Japan) Zonisamide in West syndrome Y. Suzuki (Japan) Thyrotropin-releasing hormone: role in the treatment of West syndrome and related epileptic encephalopathies Y. Takeuchi, T. Takano, J. Abe, S. Takikita, M. Ohno (Japan)

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565 570 575 580 584 586 593 603 605 609 616

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Surgical treatment of West syndrome E. Asano, D.C. Chugani, C. Juha´ sz, O. Muzik, H.T. Chugani (USA) Towards an international consensus on definitions and standardised outcome measures for therapeutic trials (and epidemiological studies) in West syndrome J.P. Osborne, A. Lux (UK) Natural History. Prognosis and Social Aspects of West Syndrome Long-term outcome of patients with West syndrome R. Riikonen (Finland) West syndrome: long-term prognosis and social aspects R.E. Appleton (UK) Long-term prognosis of patients with West syndrome in Japan: medical aspects M. Ito, T. Kumagai, Y. Yamazaki, K. Sekijima, K. Sakakibara, Y. Matsutomo, F. Hijikigawa, H. Yamada (Japan) Long-term prognosis of patients with West syndrome in Japan: social aspects T. Kumagai, M. Ito, Y. Yamazaki, K. Sekijima, K. Sakakibara, Y. Matsutomo, F. Hijikigawa, H. Yamada (Japan) Long-term follow-up study of West syndrome associated with tuberous sclerosis K. Fukushima, Y. Inoue, T. Fujiwara, K. Yagi (Japan) Spontaneous remission of spasms in West syndrome – implications of viral infection H. Hattori (Japan) Ohtahara Syndrome (EIEE) Video/EEG aspects of early-infantile epileptic encephalopathy with suppression-bursts (Ohtahara syndrome) L. Fusco, C. Pachatz, M. Di Capua, F. Vigevano (Italy) Early epileptic encephalopathy with suppression burst electroencephalographic pattern – an analysis of eight Taiwanese patients P.-T. Chen, C. Young, W.-T. Lee, P.-J. Wang, S.S. Peng, Y.-Z. Shen (Taiwan) Neuropathology of early-infantile epileptic encephalopathy with suppression-bursts; comparison with those of early myoclonic encephalopathy and West syndrome M. Itoh, S. Hanaoka, M. Sasaki, E. Ohama, S. Takashima (Japan) Surgical treatment of early-infantile epileptic encephalopathy with suppression-bursts associated with focal cortical dysplasia H. Komaki, K. Sugai, T. Maehara, H. Shimizu (Japan) Other Related Syndromes Clinical and molecular genetics of myoclonic–astatic epilepsy and severe myoclonic epilepsy in infancy (Dravet syndrome) I.E. Scheffer, R. Wallace, J.C. Mulley, S.F. Berkovic (Australia) Severe myoclonic epilepsy in infants – a review based on the Tokyo Women’s Medical University series of 84 cases H. Oguni, K. Hayashi, Y. Awaya, Y. Fukuyama, M. Osawa (Japan) Refractory grand mal seizures with onset during infancy including severe myoclonic epilepsy in infancy O. Kanazawa (Japan) Myoclonic–astatic epilepsy of early childhood – clinical and EEG analysis of myoclonic–astatic seizures, and discussions on the nosology of the syndrome H. Oguni, Y. Fukuyama, T. Tanaka, K. Hayashi, M. Funatsuka, M. Sakauchi, S. Shirakawa, M. Osawa (Japan) The PEHO syndrome R. Riikonen (Finland)

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Announcements and reports

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Instructions to authors

771

Announcements

774

Congress announcement

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Vol. 23, No. 8 Review article History of clinical identification of West syndrome – in quest after the classic Y. Fukuyama (Japan)

779

Communication Oligonucleotides against a splicing enhancer sequence led to dystrophin production in muscle cells from a Duchenne muscular dystrophy patient Y. Takeshima, H. Wada, M. Yagi, Y. Ishikawa, Y. Ishikawa, R. Minami, H. Nakamura, M. Matsuo (Japan)

788

Original articles Evaluation of autonomic nervous system function with spectral analysis of heart rate variability in a case of tetanus T. Goto, H. Fukushima, G. Sasaki, N. Matsuo, T. Takahashi (Japan)

791

Cumulative Contents to Volume 23 Mechanical ventilation care in severe childhood neurological disorders M. Sasaki, K. Sugai, M. Fukumizu, S. Hanaoka, M. Kaga (Japan) Head circumference measurement of urban children aged between 6 and 12 in Malatya, Turkey H. Karabiber, Y. Durmaz, C. Yakıncı, O. Kutlu, Y. Gumusalan, S. Yologlu, K. Yalaz (Turkey) Physical condition of preterm infants with periventricular leukomalacia A. Okumura, F. Hayakawa, T. Kato, T. Kubota, K. Maruyama, K. Itomi, K. Kuno, K. Watanabe (Japan)

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Case reports Neurological presentation of three patients with 22q11 deletion (CATCH 22 syndrome) A. Roubertie, M. Semprino, A.M. Chaze, F. Rivier, V. Humbertclaude, R. Cheminal, G. Lefort, B. Echenne (France) Molybdenum cofactor deficiency associated with Dandy–Walker complex S. Arslanoglu, M. Yalaz, D. Go¨ ks¸en, M. C ¸ oker, S. Tu¨ tu¨ ncu¨ ogˇ lu, M. Akısu, S¸ . Darcan, N. Kultursay, M. C ¸ iris¸, E. Demirtas¸ (Turkey)

810

Announcements and reports

819

Instructions to authors

820

Announcement

823

Cumulative Contents to Volume 23

824

Author Index to Volume 23

832

Subject Index to Volume 23

839

Congress announcement

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