CLINICAL GUIDELINES for CONGENITAL HEART DISEASE Contributors

CLINICAL GUIDELINES for CONGENITAL HEART DISEASE Contributors ADULT CHD CARE RESOURCES NEONATAL AND PEDIATRIC CARE RESOURCES Editor: Mary Rummell, M...
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CLINICAL GUIDELINES for CONGENITAL HEART DISEASE Contributors ADULT CHD CARE RESOURCES

NEONATAL AND PEDIATRIC CARE RESOURCES

Editor: Mary Rummell, MN, RN, CNS, CPNC Editor 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Portland, Oregon

Editors: Mary Rummell, MN, RN, CNS, CPNP, FAHA Editor 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Portland, Oregon

Contributors: Diana Arias, MSN, ARNP, FNP-C, CPN Clinical Specialist, Cardiac Intensive Care Unit Miami Children’s Hospital Miami, Florida

Dorothy M Beke, MS, RN, CPNP-PC/AC Editor 2014 and 2016 Clinical Nurse Specialist, Cardiac Intensive Care Unit Mechanical Circulatory Support Resource, Cardiac Intensive Care Unit Boston Children’s Hospital Boston Boston, Massachusetts

Kathryn Barrett, NP-C, RN, CCRN Nurse Practitioner, Pediatric Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts Loren Brown, BSN, RN, CCRN Clinical Nursing Educator, Cardiovascular Catheterization Lab Boston Children’s Hospital Boston, Massachusetts Louise Callow RN, MSN, CPNP Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan, CS Mott Children’s Center CS Mott Children’s Hospital Ann Arbor, Michigan Andrea Frederick, RN, NP Nurse Practitioner, Adult Congenital Cardiology Stanford Hospital and Clinics Palo Alto, California Annette Haynes, MS, RN, CNS, CCRN Cardiology Clinical Nurse Specialist, Stanford Hospital and Clinics Palo Alto, California Lindsey Katzmark, MSN, RN, APNP Nurse Practitioner,

Melissa B Jones, MSN, RN, APRN, CPNP-AC Editor 2016 Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Sandy Staveski, PhD, RN, CPNP-AC/PC, CNS, CCRN Editor 2014 Nurse Scientist, Research in Patient Services, Heart Institute Cincinnati Children’s Hospital Medical Center Cincinnati, Ohio Project Leads: Mary Rummell, MN, RN, CNS, CPNP, FAHA Project Lead 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Portland, Oregon Dorothy M Beke, RN, MS, CPNP-PC/AC Project Lead 2014 and 2016 Clinical Nurse Specialist, Cardiac Intensive Care Unit Mechanical Circulatory Support Resource, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts 1

Adult Congenital Heart Disease Program Children’s Hospital of Wisconsin Milwaukee, Wisconsin Mary Rummell, MN, RN, CNS, CPNP, FAHA Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Portland, Oregon Jo Ann Nieves, MSN, CPN, ARNP, PNP-BC Nurse Practitioner, Adult Congenital Heart Program Miami Children’s Hospital Miami, Florida Nancy Rudd, MS, RN, CPNP-AC/PC Nurse Practitioner, Pediatric Cardiology Adult Congenital Heart Disease Program Children’s Hospital of Wisconsin Milwaukee, Wisconsin Margaret Schroder, RN, PNP-BC Nurse Practitioner, Cardiovascular Surgery Boston Children’s Hospital Boston, Massachusetts Services, Heart Institute Sandy Staveski, PhD, RN, CPNP-AC/PC, CNS, CCRN Nurse Scientist, Research in Patient Services, Heart Institute Cincinnati Children’s Hospital Medical Center Cincinnati, Ohio

Melissa B Jones, MSN, RN, APRN, CPNP-AC Project Lead 2016 Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Christine Riley, MSN, APRN, CPNP-AC Project Lead 2016 Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Louise Callow, MSN, RN, CPNP Project Lead 2014 and 2016 Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan Congenital Heart Hospital Ann Arbor, Michigan Cecilia St. George-Hyslop, M Ed, BScN, RN, CNCCP (C) Project Lead 2014 and 2016 Advanced Nursing Practice Educator Cardiac Intensive Care Unit The Labatt Family Heart Centre The Hospital for Sick Children Toronto, Ontario, Canada Bronwyn Bartle, DNP, CPNP-AC/PC Project Lead 2016 Pediatric Nurse Practitioner, Duke Children’s Pediatric and Congenital Heart Center Durham, North Carolina Dawn Tucker MSN, RN, CPNP-AC Project Lead 2014 Director, Heart Center Advanced Practice Nurse, Cardiac Intensive Care Unit Children’s Mercy Hospital and Clinics Kansas City, Missouri Contributors: Luisa F. Angel, ARNP, PPCNP-BC Nurse Practitioner , Cardiac Intensive Care Unit Nicklaus Children’s Hospital Heart Program Miami, Florida Annierose D. Abogadie BSN, RN, CCRN, RN-BC Clinical Manger, Cardiac Intensive Care Unit Children’s National Health System 2

Washington, DC Catherine Baxter, MSN, RN, CPNP-AC Pediatric Nurse Practitioner, Pediatric Cardiac Surgery Levine Children’s Hospital Charlotte, North Carolina Dorothy M Beke, RN, MS, CPNP-PC/AC Clinical Nurse Specialist, Cardiac Intensive Care Unit Mechanical Circulatory Support Resource, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts Angela Blankenship, RN, MS, CPNP-PC/AC Nurse Practitioner, Cardiac Intensive Care Unit Nationwide Children’s Hospital Columbus, Ohio Lindsey Bradbury, BSN, RN, CCRN Nursing Department Director, Pediatric Intensive Care Unit Children’s Mercy Hospitals and Clinics Kansas City, Missouri Erin Burke, MSN, RN, PNP Nurse Practitioner , Cardiology Preoperative Clinic Boston Children’s Hospital Boston, MA Patricia Burke, BSN, CCRN Staff Nurse III, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, MA Louise Callow, MSN, RN, CPNP Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan, CS Mott Children’s Hospital Ann Arbor, Michigan Christine Chiu-Man, MSc, RCT, RCES, CEPS, CCDS, FHRS Team Lead, EP Pacemaker Technologist Hospital for Sick Children Toronto, Canada Jason Corcoran, PharmD, BCPS Manager, Clinical Pharmacy Services, Clinical Specialist, Cardiac Intensive Care Unit Children’s National Health System 3

Washington, DC Meghan Cusick, MSN, RN, NP-C Nurse Practitioner , Cardiology Preoperative Clinic Boston Children’s Hospital Boston, MA Elizabeth S Daley, BSN, RN, BA, CCRN Staff Nurse III, Cardiothoracic Intensive Care Unit Children’s Hospital of Los Angeles Los Angeles, California T. Lynn Dees, MNSc, APRN, PNP-BC, CPNP-AC Advanced Practice Nurse, Pediatric Cardiology University of Arkansas for Medical Sciences Arkansas Children’s Hospital Little Rock, Arkansas Amy Donnellan, MSN, CPNP-AC Clinical Nurse Specialist, Cardiac Intensive Care Unit Cincinnati Children’s Hospital Medical Center Cincinnati, Ohio Misty Ellis, MSN, APRN Pediatric Nurse Practitioner, University of Louisville and Kosair Children’s Hospital Department of Pediatric Critical Care Louisville, Kentucky Andrea Frederick, NP Nurse Practitioner, Adult Congenital Cardiology, Stanford Hospital and Clinics Stanford, California (original author) Amanda Green, MSN, ARNP, FNP-C Nurse Practitioner, Cardiac Catheterization Laboratory Nicklaus Children’s Hospital Miami, Florida Melanie Guerrero, MSN, RN, CPN Patient Care Services Clinical Manager, Cardiovascular Acute Unit Children’s Hospital Los Angeles Los Angelis, California Nancy Hagberg, MS, RN, FNP Nurse Practitioner, Child Heart Associates 4

Worcester, Massachusetts Ashley Harlow, BSN, RN, CCRN Clinical Educator, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Jenna Heichel, MSN, APRN, CPNP-AC Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Flerida Imperial-Perez, MN, RN, CNS-BC, CCNS-P Patient Care Services Clinical Manager, Clinical Nurse Specialist Cardiothoracic Intensive Care Unit Children’s Hospital Los Angeles Los Angelis, California Melissa B Jones, MSN, RN, APRN, CPNP-AC Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Lindsey Justice, MSN, RN, CPNP-AC Nurse Practitioner, Cardiac Intensive Care Unit Cincinnati Children’s Hospital Medical Center Cincinnati, Ohio Kim Kellogg, MS, RN, CPNP Pediatric Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan Congenital Heart Center CS Mott Children’s Hospital Ann Arbor, Michigan Jeannie Koo, RN, CPNP-AC Nurse Practitioner, Pediatric Critical Care Duke Children’s Hospital Durham, North Carolina Linda M. Lambert, MSN, RN, CFNP Nurse Practitioner, Pediatric Cardiothoracic Surgery Primary Children’s Hospital Salt Lake City, Utah Patricia Lincoln, MS, RN, CCRN, CNS-BC Clinical Nurse Specialist, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts 5

Grace Macek, MSN, RN, PNP-BC Pediatric Nurse Practitioner, Cardiac and Thoracic Surgery University of Chicago Medicine, Comer Children’s Hospital Chicago, Illinois Megan Matiasek, MS, RN, CPNP-PC/AC Nurse Practitioner, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts Sandra McGill-Lane, MSN,RN, FNP, CCRN Clinical Nurse Specialist, Pediatric Cardiac Intensive Care Unit Morgan Stanley’s Children’s Hospital of New York Presbyterian New York, New York Amber Merritt, MSN, RN, RN-BC, CCRN Clinical Coordinator, Cardiac Intensive Care Unit Children’s Hospital Los Angeles Los Angeles, California Justine Mize, MSN, RN, CCRN, CPN Professional Practice Specialist, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Debra Forbes Morrow, BSN, RN, CCRN Staff Nurse Level III, Cardiac Intensive Care Unit Infection Prevention Coordinator, Cardiac Intensive Care Unit Children’s Hospital Boston Boston, Massachusetts Candace Morton, MSN, RN, APNP Pediatric Nurse Practitioner, Electrophysiology Children’s Hospital of Wisconsin Milwaukee, Wisconsin Catherine Murphy, BSN, RN Staff Nurse, Cardiac Critical Care Unit Labatt Family Heart Center Hospital for Sick Children Toronto, Canada 6

Jenna Murray, MSN, RN, CPNP-AC Ventricular Assist Device Coordinator/ Heart Failure Nurse Practitioner Lucile Packard Children’s Hospital Stanford Palo Alto, California Casey Naughton, MS, RN, BSN, CPNP-AC Nurse Practitioner, Children’s Heart Program University of Maryland Medical Center Baltimore, Maryland Jennifer Newcombe, MSN, CNS, CPNP-PC/AC Nurse Practitioner, Pediatric Cardiothoracic Surgery Loma Linda University Hospital Loma Linda, California Jo Ann Nieves, MSN, CPN, ARNP, PNP-BC, FAHA Nurse Practitioner, Cardiology Nicklaus Children’s Hospital Miami, Florida Melissa Olen, MSN, ARPN, FNP-C, CCRN Electrophysiology Nurse Practitioner, Coordinator of Remote Device Clinic Nicklaus Children’s Hospital Miami, Florida Nida Oriza, RN, BSN Core Charge Nurse, Cardiac Intensive Care Unit Children’s Hospital Los Angeles Los Angeles, California Emily Peterson, RN, NP Nurse Practitioner, Cardiac Intensive Care Unit Lurie Children’s Hospital Chicago, Illinois Courtney Petro, RN , BSN, CCRN Staff Nurse, Pediatric Cardiac Intensive Care Unit Lucile Packard Children’s Hospital at Stanford Palo Alto, California Nida Sulit-Oriza, BSN, RN Clinical Nurse IV, Core Charge Nurse Cardiothoracic Intensive Care Unit Children’s Hospital Los Angeles Los Angeles, California

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Christine M. Rachwal, MSN, RN, CCRN Clinical Nurse Specialist, Cardiac Intensive Care Unit Boston Children’s Hospital Boston, Massachusetts Christine Riley, MSN, APRN, CPNP-AC Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Kaye Remo, RN Staff Nurse, Cardiac Intensive Care Unit University of California San Francisco Benioff Children’s Hospital San Francisco, California Gwen Rempel, PhD, RN Associate Professor, Faculty of Health Disciplines Athabasca University Associate Adjunct Professor, Faculty of Nursing, University of Alberta Associate Adjunct Professor, Department of Pediatrics, University of Alberta Alberta, Canada Christine Riley, MSN, APRN, CPNP-AC Nurse Practitioner, Cardiac Intensive Care Unit Children’s National Health System Washington, DC Mary Rummell, MN, RN, CPNP, CNS, FAHA Clinical Nurse Specialist, Pediatric Cardiology, Cardiac Services Oregon Health & Science University (Retired) Portland, Oregon Melanie Sojka, MSN, RN, CPNP-AC/PC Advanced Practice Nurse/Pediatric Nurse Practitioner, Pediatric Cardiac Surgery University of Chicago Medicine, Comer Children’s Hospital Chicago, Illinois Jennifer Strawn, BSN, RN, CPN Nurse Clinician, Pediatric Cardiology Children’s Hospital & Medical Center Omaha, Nebraska Cecelia St. George-Hyslop, M Ed, RN, BA Gen, CNCCPC 8

Advanced Practice Nurse Educator, Cardiac Critical Care Unit Labatt Family Heart Center Hospital for Sick Children Toronto, Canada Svetlana Streltsova MSN, RN, CCRN Clinical Nurse III, Pediatric Cardiac Intensive Care Unit Morgan Stanley Children’s Hospital of New York Presbyterian New York, New York Kristen Sullivan, MSN, RN, CPNP-AC Nurse Practitioner, Cardiothoracic Surgery Phoenix Children’s Hospital Heart Center Phoenix, Arizona Alisa Tortorich, RD, CSP, CNSC, LD Board Certified Specialist in Pediatric Nutrition Certified Nutrition Support Clinician Doernbecher Children’s Hospital Portland, Oregon Victoria Winter, RN, MSN, CNS, CCRN Clinical Nurse IV, Cardiothoracic Intensive Care Unit Children’s Hospital Los Angeles Los Angeles, California Adjunct Professor Azusa Pacific University School of Nursing Azusa, California

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